Primary defect of juvenile visceral steatosis (jvs) mouse with systemic carnitine deficiency is probably in renal carnitine transport system
about
Primary systemic carnitine deficiency is caused by mutations in a gene encoding sodium ion-dependent carnitine transporterDevelopment and characterization of an animal model of carnitine deficiencyDysfunctions of the epididymis as a result of primary carnitine deficiency in juvenile visceral steatosis miceA mutation in SLC22A4 encoding an organic cation transporter expressed in the cochlea strial endothelium causes human recessive non-syndromic hearing loss DFNB60Carnitine biosynthesis in mammals.Role of carnitine in the regulation of glucose homeostasis and insulin sensitivity: evidence from in vivo and in vitro studies with carnitine supplementation and carnitine deficiency.Transcriptional regulation of genes for ornithine cycle enzymes.Usefulness of kidney slices for functional analysis of apical reabsorptive transporters.A novel gene suppressed in the ventricle of carnitine-deficient juvenile visceral steatosis mice.Characterization of the endogenous carnitine transport and expression of a rat renal Na(+)-dependent carnitine transport system in Xenopus laevis oocytes.Characterization of L-carnitine transport by rat kidney brush-border-membrane vesicles.Effect of gamma-butyrobetaine on fatty liver in juvenile visceral steatosis mice.Effect of carnitine deprivation on carnitine homeostasis and energy metabolism in mice with systemic carnitine deficiency.Contractile function and energy metabolism of skeletal muscle in rats with secondary carnitine deficiency.Inhibited Carnitine Synthesis Causes Systemic Alteration of Nutrient Metabolism in Zebrafish.
P2860
Q22008704-225DA7A0-AC45-4AA1-96A6-A76594E74548Q28204749-45F34E3C-8813-4065-BF10-BFB883399292Q28591160-3E7BDE31-5286-4062-8F4E-3C846B23C88DQ30357625-A93AF445-3B80-4AA9-919C-ECF94AD8C6C3Q34501779-F363F1CE-5B3E-4FD1-AD46-2DD3FB37F4F7Q37963740-7996BA51-5133-4A41-A6F0-3CDD556D76CFQ40941734-31263098-7509-4F0A-91B9-59DFA6891420Q42373933-AB7AFC94-4FB0-4D61-9969-5EDDFA195D4DQ42658347-1240E341-4A1D-43D0-8DF6-9C8A6579E37CQ42821496-52BFE40B-00E8-4134-BC9F-57366E2DBBBBQ42821572-5BFC84A2-17E1-456D-871C-E91D30EADB37Q43600013-1EBB19DE-AE89-4B44-9A54-E4C454202FD6Q46640601-01A811D3-5B23-4510-96D9-BEA8896AEF8BQ47695141-41377845-B639-4D9E-AA31-30E842F2749AQ55012104-6D4568E3-FEA0-47D1-B9C0-EF21E83E369D
P2860
Primary defect of juvenile visceral steatosis (jvs) mouse with systemic carnitine deficiency is probably in renal carnitine transport system
description
1994 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
1994 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
artículu científicu espublizáu en 1994
@ast
im April 1994 veröffentlichter wissenschaftlicher Artikel
@de
scientific journal article
@en
vedecký článok (publikovaný 1994/04/12)
@sk
vědecký článek publikovaný v roce 1994
@cs
wetenschappelijk artikel (gepubliceerd op 1994/04/12)
@nl
наукова стаття, опублікована у квітні 1994
@uk
научни чланак (објављен 1994/04/12)
@sr
name
Primary defect of juvenile vis ...... nal carnitine transport system
@ast
Primary defect of juvenile vis ...... nal carnitine transport system
@en
Primary defect of juvenile vis ...... nal carnitine transport system
@nl
type
label
Primary defect of juvenile vis ...... nal carnitine transport system
@ast
Primary defect of juvenile vis ...... nal carnitine transport system
@en
Primary defect of juvenile vis ...... nal carnitine transport system
@nl
prefLabel
Primary defect of juvenile vis ...... nal carnitine transport system
@ast
Primary defect of juvenile vis ...... nal carnitine transport system
@en
Primary defect of juvenile vis ...... nal carnitine transport system
@nl
P2093
P1476
Primary defect of juvenile vis ...... nal carnitine transport system
@en
P2093
H. Nikaido
J. Hayakawa
K. Kobayashi
M. Horiuchi
M. Kuwajima
N. Shimizu
S. Yamaguchi
T. Koizumi
P356
10.1016/0925-4439(94)90054-X
P407
P577
1994-04-12T00:00:00Z