LRPPRC mutation suppresses cytochrome oxidase activity by altering mitochondrial RNA transcript stability in a mouse model
about
Copper supplementation restores cytochrome c oxidase assembly defect in a mitochondrial disease model of COA6 deficiencyAccessorizing the human mitochondrial transcription machineryThe Pet309 pentatricopeptide repeat motifs mediate efficient binding to the mitochondrial COX1 transcript in yeast.Transcription-independent role for human mitochondrial RNA polymerase in mitochondrial ribosome biogenesisThe elusive nature of adaptive mitochondrial DNA evolution of an arctic lineage prone to frequent introgression.Mitochondrial Diseases Part II: Mouse models of OXPHOS deficiencies caused by defects in regulatory factors and other components required for mitochondrial function.Coiled coil domain-containing protein 56 (CCDC56) is a novel mitochondrial protein essential for cytochrome c oxidase functionMitochondrion-associated protein LRPPRC suppresses the initiation of basal levels of autophagy via enhancing Bcl-2 stability.Mitochondrial transcription: lessons from mouse models.Human pentatricopeptide proteins: only a few and what do they do?Elevated levels of mitochondrion-associated autophagy inhibitor LRPPRC are associated with poor prognosis in patients with prostate cancer.Loss of LRPPRC causes ATP synthase deficiencyMouse models for mitochondrial diseases.Tissue- and species-specific differences in cytochrome c oxidase assembly induced by SURF1 defects.MRPS27 is a pentatricopeptide repeat domain protein required for the translation of mitochondrially encoded proteins.Increased Hepatic Fatty Acids Uptake and Oxidation by LRPPRC-Driven Oxidative Phosphorylation Reduces Blood Lipid Levels.Mitochondrial dysfunction and ovarian aging.The emerging role of immune dysfunction in mitochondrial diseases as a paradigm for understanding immunometabolism.
P2860
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P2860
LRPPRC mutation suppresses cytochrome oxidase activity by altering mitochondrial RNA transcript stability in a mouse model
description
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
artikull shkencor
@sq
artículu científicu espublizáu en 2012
@ast
im Januar 2012 veröffentlichter wissenschaftlicher Artikel
@de
scientific journal article
@en
wetenschappelijk artikel
@nl
наукова стаття, опублікована в січні 2012
@uk
مقالة علمية (نشرت عام 2012)
@ar
name
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@ast
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@en
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@nl
type
label
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@ast
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@en
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@nl
prefLabel
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@ast
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@en
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@nl
P2093
P2860
P3181
P356
P1433
P1476
LRPPRC mutation suppresses cyt ...... ipt stability in a mouse model
@en
P2093
Brian H. Robinson
Fenghao Xu
Jane B. L. Addis
Jessie M. Cameron
P2860
P304
P3181
P356
10.1042/BJ20110985
P407
P577
2012-01-01T00:00:00Z