LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells.
about
A mutation in the human CBP4 ortholog UQCC3 impairs complex III assembly, activity and cytochrome b stabilityC11orf83, a mitochondrial cardiolipin-binding protein involved in bc1 complex assembly and supercomplex stabilizationIron-sulfur cluster biogenesis in mammalian cells: New insights into the molecular mechanisms of cluster deliveryMitochondrial Protein Interaction Mapping Identifies Regulators of Respiratory Chain FunctionRespiratory chain complex III deficiency due to mutated BCS1L: a novel phenotype with encephalomyopathy, partially phenocopied in a Bcs1l mutant mouse model.Parallel evolution of genes controlling mitonuclear balance in short-lived annual fishesA homozygous mutation in LYRM7/MZM1L associated with early onset encephalopathy, lactic acidosis, and severe reduction of mitochondrial complex III activity.Polymerase I and transcript release factor (PTRF) regulates adipocyte differentiation and determines adipose tissue expandability.Eukaryotic LYR Proteins Interact with Mitochondrial Protein ComplexesMammalian Fe-S proteins: definition of a consensus motif recognized by the co-chaperone HSC20Nuclear gene mutations as the cause of mitochondrial complex III deficiencyMitochondria and Iron: current questions.COX7A2L Is a Mitochondrial Complex III Binding Protein that Stabilizes the III2+IV Supercomplex without Affecting Respirasome Formation.LYRM7 mutations cause a multifocal cavitating leukoencephalopathy with distinct MRI appearance.The superfamily of mitochondrial Complex1_LYR motif-containing (LYRM) proteins.Severe respiratory complex III defect prevents liver adaptation to prolonged fasting.Mitochondrial complex III Rieske Fe-S protein processing and assembly.Quantitative proteomic study of myocardial mitochondria in urea transporter B knockout mice.Assembly of mammalian oxidative phosphorylation complexes I-V and supercomplexes
P2860
03abe3f55c2ec23d746499c368e441349d4bca5c053acebe0bbb4c96f4307c575e652ec30ab7dd9305d1d3e96c980e42691ed9c963f6cf458771430d151a1a2cb512a20134de45d3e956ebdf9cf8a77d8d411427e21f7236585418b2c82e3bbb976ffa12a6c1af527a83103d8e0939a1dfc8d0bca7b9fa1ba7ee8cd738a5a27b409ce30915fdb53801592d33af7c943ec0e93292070bbdc781646fd9fc926d5fbb933d0193b625d8f1917f4144ea7430e15391f5
P248
Q24300577-42A4B56F-8E69-499F-AE32-0430E771CA3CQ24315727-E478F83F-2314-43F6-BBC4-791B255BC7A2Q26850111-BD9E8F26-9619-44CE-9049-FCFF1DA75C43Q28117113-23F0FF3F-B4B6-4F2D-ABF1-7B0CF035E874Q30846636-8ADFF4B3-CB86-44F0-A519-1BC18D9CF0D2Q33638908-3FA1911B-C3EA-41F9-9606-E018F806F9CCQ33641802-1AC39BD2-D24B-48CB-BA38-09DE908799F2Q33913173-324362DB-FF27-41D4-AE1C-2C81257BF4CAQ35237404-EA3CF854-7C37-4257-9AEE-2494648E3860Q37590176-B07447F6-1DFC-4E68-8EB5-19C83A4B08F9Q38443565-84601A5D-F9BE-4380-B2D0-A8875976AD5FQ39027015-83BF1389-CB80-464C-9936-788BBD503C87Q39469342-3491EF29-6673-4C05-A92B-0B3F252DAD7EQ39970753-40FC9016-BA55-433E-9CBB-0D8DE12BBE8BQ44706313-C7999CBB-93E1-46D8-A296-9537B3C8D038Q46869930-A74D7EEC-5F47-4D3D-9253-561DF34AC176Q47290712-96013B32-0830-4DE5-8062-89BA8E477C75Q51709308-D5936702-87DA-4ADB-8CCD-C65ABF9FF1E9Q56760543-901BDF4D-7345-497C-9B6F-28BEAD33427A
P2860
LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells.
description
2012 nî lūn-bûn
@nan
2012 թուականի Նոյեմբերին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի նոյեմբերին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@ast
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@en
type
label
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@ast
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@en
prefLabel
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@ast
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@en
P2093
P2860
P921
P1476
LYRM7/MZM1L is a UQCRFS1 chape ...... x III assembly in human cells.
@en
P2093
Dennis R Winge
Erika Fernández-Vizarra
Ester Sánchez
Jennifer L Fox
Teresa Lobo
P2860
P304
P356
10.1016/J.BBABIO.2012.11.003
P407
P577
2012-11-17T00:00:00Z