Dominant-negative action of the jimpy mutation in mice complemented with an autosomal transgene for myelin proteolipid protein.
about
Chemical deacylation reduces the adhesive properties of proteolipid protein and leads to decompaction of the myelin sheath.CNS myelination and PLP gene dosage.The unfolded protein response modulates disease severity in Pelizaeus-Merzbacher disease.Disrupted proteolipid protein trafficking results in oligodendrocyte apoptosis in an animal model of Pelizaeus-Merzbacher disease.The molecular and cellular defects underlying Pelizaeus-Merzbacher disease.Phylogeny of proteolipid proteins: divergence, constraints, and the evolution of novel functions in myelination and neuroprotection.Cellular Pathology of Pelizaeus-Merzbacher Disease Involving Chaperones Associated with Endoplasmic Reticulum StressProgesterone antagonist therapy in a Pelizaeus-Merzbacher mouse model.Endoplasmic Reticulum Protein Quality Control Failure in Myelin Disorders.Trafficking of PLP/DM20 and cAMP signaling in immortalized jimpy oligodendrocytes.An immortalized jimpy oligodendrocyte cell line: defects in cell cycle and cAMP pathway.Phenotypic severity of murine Plp mutants reflects in vivo and in vitro variations in transport of PLP isoproteins.Peripheral Neuropathy Caused by Proteolipid Protein Gene Mutations.Current concepts of PLP and its role in the nervous system.Mouse models of myelin diseases.Animal models of demyelination.Identification of GPM6A and GPM6B as potential new human lymphoid leukemia-associated oncogenes.Transgenic and natural mouse models of proteolipid protein (PLP)-related dysmyelination and demyelination.
P2860
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P2860
Dominant-negative action of the jimpy mutation in mice complemented with an autosomal transgene for myelin proteolipid protein.
description
1995 nî lūn-bûn
@nan
1995 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
1995 թվականի մայիսին հրատարակված գիտական հոդված
@hy
1995年の論文
@ja
1995年論文
@yue
1995年論文
@zh-hant
1995年論文
@zh-hk
1995年論文
@zh-mo
1995年論文
@zh-tw
1995年论文
@wuu
name
Dominant-negative action of th ...... or myelin proteolipid protein.
@ast
Dominant-negative action of th ...... or myelin proteolipid protein.
@en
Dominant-negative action of th ...... or myelin proteolipid protein.
@nl
type
label
Dominant-negative action of th ...... or myelin proteolipid protein.
@ast
Dominant-negative action of th ...... or myelin proteolipid protein.
@en
Dominant-negative action of th ...... or myelin proteolipid protein.
@nl
prefLabel
Dominant-negative action of th ...... or myelin proteolipid protein.
@ast
Dominant-negative action of th ...... or myelin proteolipid protein.
@en
Dominant-negative action of th ...... or myelin proteolipid protein.
@nl
P2093
P2860
P356
P1476
Dominant-negative action of th ...... or myelin proteolipid protein.
@en
P2093
Griffiths IR
Readhead C
Schneider AM
P2860
P304
P356
10.1073/PNAS.92.10.4447
P407
P577
1995-05-01T00:00:00Z