DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
about
Hallmarks of progeroid syndromes: lessons from mice and reprogrammed cellsMolecular insights into the premature aging disease progeriaThe germline/soma dichotomy: implications for aging and degenerative diseaseRecent advances in understanding the role of lamins in health and diseaseGenetics of inherited cardiocutaneous syndromes: a reviewPhysiological and Pathological Aging Affects Chromatin Dynamics, Structure and Function at the Nuclear EdgeProgerin sequestration of PCNA promotes replication fork collapse and mislocalization of XPA in laminopathy-related progeroid syndromes.Lamins in the nuclear interior - life outside the lamina.Expression of progerin does not result in an increased mutation rate.Tying up loose ends: telomeres, genomic instability and lamins.The nuclear lamina in health and disease.Fanconi Anemia: A DNA repair disorder characterized by accelerated decline of the hematopoietic stem cell compartment and other features of aging.Hutchinson-Gilford Progeria Syndrome: A premature aging disease caused by LMNA gene mutations.A decade of understanding spatio-temporal regulation of DNA repair by the nuclear architecture.The pathological consequences of impaired genome integrity in humans; disorders of the DNA replication machinery.Vitamin D receptor signaling improves Hutchinson-Gilford progeria syndrome cellular phenotypes.A Tissue Engineered Blood Vessel Model of Hutchinson-Gilford Progeria Syndrome Using Human iPSC-derived Smooth Muscle CellsDNA replication timing alterations identify common markers between distinct progeroid diseases.Emerging candidate treatment strategies for Hutchinson-Gilford progeria syndrome.A Cell-Intrinsic Interferon-like Response Links Replication Stress to Cellular Aging Caused by Progerin.Differential stem cell aging kinetics in Hutchinson-Gilford progeria syndrome and Werner syndrome.Mice with reduced expression of the telomere-associated protein Ft1 develop p53-sensitive progeroid traits.
P2860
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P2860
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
description
2015 nî lūn-bûn
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2015 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2015 թվականի հունիսին հրատարակված գիտական հոդված
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2015年の論文
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2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
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name
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@ast
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@en
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@nl
type
label
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@ast
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@en
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@nl
prefLabel
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@ast
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@en
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome.
@nl
P2860
P1476
DNA repair defects and genome instability in Hutchinson-Gilford Progeria Syndrome
@en
P2093
Ray Kreienkamp
Susana Gonzalo
P2860
P356
10.1016/J.CEB.2015.05.007
P577
2015-06-12T00:00:00Z