Cone opsin determines the time course of cone photoreceptor degeneration in Leber congenital amaurosis.
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Pharmacological Amelioration of Cone Survival and Vision in a Mouse Model for Leber Congenital AmaurosisDamage of photoreceptor-derived cells in culture induced by light emitting diode-derived blue lightPathophysilogical mechanism and treatment strategies for Leber congenital amaurosis.Endoplasmic reticulum stress and the unfolded protein responses in retinal degeneration.QLT091001, a 9-cis-retinal analog, is well-tolerated by retinas of mice with impaired visual cycles.Inhibition of thyroid hormone receptor locally in the retina is a therapeutic strategy for retinal degeneration.Protection of retina by mini-αA in NaIO3-induced retinal pigment epithelium degeneration mice.Autophagy supports survival and phototransduction protein levels in rod photoreceptors.Genetic deletion of S-opsin prevents rapid cone degeneration in a mouse model of Leber congenital amaurosisGene therapy rescues photoreceptor blindness in dogs and paves the way for treating human X-linked retinitis pigmentosa.Endoplasmic reticulum stress-associated cone photoreceptor degeneration in cyclic nucleotide-gated channel deficiency.M-opsin protein degradation is inhibited by MG-132 in Rpe65⁻/⁻ retinal explant cultureCorrelation of ER stress and retinal degeneration in tubby mice.Activation of glucocorticoid receptors in Müller glia is protective to retinal neurons and suppresses microglial reactivity.Complementation test of Rpe65 knockout and tvrm148.Noncanonical autophagy promotes the visual cycleEarly degeneration of photoreceptor synapse in Ccl2/Cx3cr1-deficient mice on Crb1(rd8) backgroundDimerization of visual pigments in vivo.Immuno-histochemical analysis of rod and cone reaction to RPE65 deficiency in the inferior and superior canine retina.The Degeneration and Apoptosis Patterns of Cone Photoreceptors in rd11 Mice.Suppressing thyroid hormone signaling preserves cone photoreceptors in mouse models of retinal degeneration.Ablation of EYS in zebrafish causes mislocalisation of outer segment proteins, F-actin disruption and cone-rod dystrophy.The involvement of ATF4 and S-opsin in retinal photoreceptor cell damage induced by blue LED light.Lecithin:Retinol Acyltransferase: A Key Enzyme Involved in the Retinoid (visual) Cycle.Role of endoplasmic reticulum stress in light-induced photoreceptor degeneration in mice.Chemical chaperone TUDCA preserves cone photoreceptors in a mouse model of Leber congenital amaurosis.A Phe-rich region in short-wavelength sensitive opsins is responsible for their aggregation in the absence of 11-cis-retinal.Autosomal recessive retinitis pigmentosa E150K opsin mice exhibit photoreceptor disorganization.RPE65 gene therapy slows cone loss in Rpe65-deficient dogs.A subpopulation of activated retinal macrophages selectively migrated to regions of cone photoreceptor stress, but had limited effect on cone death in a mouse model for type 2 Leber congenital amaurosis.Severe Loss of Tritan Color Discrimination in RPE65 Associated Leber Congenital Amaurosis.Endoplasmic reticulum (ER) Ca2+-channel activity contributes to ER stress and cone death in cyclic nucleotide-gated channel deficiency.Disruption of Rhodopsin Dimerization in Mouse Rod Photoreceptors by Synthetic Peptides Targeting Dimer Interface.Evaluation of Congo Red Staining in Degenerating Porcine Photoreceptors In Vitro: Protective Effects by Structural and Trophic Support.Analysis of the bystander effect in cone photoreceptors via a guided neural network platform.
P2860
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P2860
Cone opsin determines the time course of cone photoreceptor degeneration in Leber congenital amaurosis.
description
2011 nî lūn-bûn
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2011 թուականի Մայիսին հրատարակուած գիտական յօդուած
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2011 թվականի մայիսին հրատարակված գիտական հոդված
@hy
2011年の論文
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2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Cone opsin determines the time ...... in Leber congenital amaurosis.
@ast
Cone opsin determines the time ...... in Leber congenital amaurosis.
@en
type
label
Cone opsin determines the time ...... in Leber congenital amaurosis.
@ast
Cone opsin determines the time ...... in Leber congenital amaurosis.
@en
prefLabel
Cone opsin determines the time ...... in Leber congenital amaurosis.
@ast
Cone opsin determines the time ...... in Leber congenital amaurosis.
@en
P2093
P2860
P356
P1476
Cone opsin determines the time ...... in Leber congenital amaurosis.
@en
P2093
Ning Zhang
Wolfgang Baehr
Yingbin Fu
P2860
P304
P356
10.1073/PNAS.1017127108
P407
P577
2011-05-09T00:00:00Z