Ammonia control and neurocognitive outcome among urea cycle disorder patients treated with glycerol phenylbutyrate.
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Randomized, double-blind, controlled study of glycerol phenylbutyrate in hepatic encephalopathy.Switch from Sodium Phenylbutyrate to Glycerol Phenylbutyrate Improved Metabolic Stability in an Adolescent with Ornithine Transcarbamylase DeficiencyUrinary phenylacetylglutamine (U-PAGN) concentration as biomarker for adherence in patients with urea cycle disorders (UCD) treated with glycerol phenylbutyrate.Elevated phenylacetic acid levels do not correlate with adverse events in patients with urea cycle disorders or hepatic encephalopathy and can be predicted based on the plasma PAA to PAGN ratio.Results from a Nationwide Cohort Temporary Utilization Authorization (ATU) survey of patients in france treated with Pheburane(®) (Sodium Phenylbutyrate) taste-masked granules.Blood ammonia and glutamine as predictors of hyperammonemic crises in patients with urea cycle disorder.Glutamine and hyperammonemic crises in patients with urea cycle disorders.Postanalytical tools improve performance of newborn screening by tandem mass spectrometry.Glycerol phenylbutyrate treatment in children with urea cycle disorders: pooled analysis of short and long-term ammonia control and outcomes.Nicotine replacement therapy in the intensive care unit: a systematic review.A novel mutation in ornithine transcarbamylase gene causing mild intermittent hyperammonemiaExecutive functioning profiles from the BRIEF across pediatric medical disorders: Age and diagnosis factors.Refeeding syndrome in a young woman with argininosuccinate lyase deficiencyProtein and calorie intakes in adult and pediatric subjects with urea cycle disorders participating in clinical trials of glycerol phenylbutyrate.Self-reported treatment-associated symptoms among patients with urea cycle disorders participating in glycerol phenylbutyrate clinical trials.Population pharmacokinetic modeling and dosing simulations of nitrogen-scavenging compounds: disposition of glycerol phenylbutyrate and sodium phenylbutyrate in adult and pediatric patients with urea cycle disordersLong-Term Follow-Up on a Cohort Temporary Utilization Authorization (ATU) Survey of Patients Treated with Pheburane (Sodium Phenylbutyrate) Taste-Masked Granules.Targeting CPS1 in the treatment of Carbamoyl phosphate synthetase 1 (CPS1) deficiency, a urea cycle disorder.A cross-sectional multicenter study of osteogenesis imperfecta in North America - results from the linked clinical research centers.Profile of sodium phenylbutyrate granules for the treatment of urea-cycle disorders: patient perspectives.Late-onset ornithine carbamoyltransferase deficiency accompanying acute pancreatitis and hyperammonemia.Orally administered sodium 4-phenylbutyrate suppresses the development of dextran sulfate sodium-induced colitis in mice.
P2860
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P2860
Ammonia control and neurocognitive outcome among urea cycle disorder patients treated with glycerol phenylbutyrate.
description
2013 nî lūn-bûn
@nan
2013年の論文
@ja
2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
@wuu
2013年论文
@zh
2013年论文
@zh-cn
name
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@ast
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@en
type
label
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@ast
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@en
prefLabel
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@ast
Ammonia control and neurocogni ...... with glycerol phenylbutyrate.
@en
P2093
P2860
P50
P356
P1433
P1476
Ammonia control and neurocogni ...... d with glycerol phenylbutyrate
@en
P2093
Annette Feigenbaum
Brendan Lee
Bruce F Scharschmidt
Cary O Harding
Cynthia Lemons
David Kronn
Dennis Bartholomew
Dion F Coakley
George A Diaz
James Bartley
P2860
P304
P356
10.1002/HEP.26058
P407
P577
2013-01-03T00:00:00Z