Non-native soluble oligomers of Cu/Zn superoxide dismutase (SOD1) contain a conformational epitope linked to cytotoxicity in amyotrophic lateral sclerosis (ALS).
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Identification of a misfolded region in superoxide dismutase 1 that is exposed in amyotrophic lateral sclerosis.Aggregation propensities of superoxide dismutase G93 hotspot mutants mirror ALS clinical phenotypesThe effect of amyotrophic lateral sclerosis-linked exogenous SOD1-G93A on electrophysiological properties and intracellular calcium in cultured rat astrocytes.A model for non-obligate oligomer formation in protein aggregration.Nonnative SOD1 trimer is toxic to motor neurons in a model of amyotrophic lateral sclerosis.ALS-linked misfolded SOD1 species have divergent impacts on mitochondria.A Phosphomimetic Mutation Stabilizes SOD1 and Rescues Cell Viability in the Context of an ALS-Associated Mutation.Spinal cord homogenates from SOD1 familial amyotrophic lateral sclerosis induce SOD1 aggregation in living cells.A mechanism for propagated SOD1 misfolding from frustration analysis of a G85R mutant protein assembly.Disulfide cross-linked multimers of TDP-43 and spinal motoneuron loss in a TDP-43A315T ALS/FTD mouse model.An in silico study of the effect of SOD1 electrostatic loop dynamics on amyloid‑like filament formation.Large SOD1 aggregates, unlike trimeric SOD1, do not impact cell viability in a model of amyotrophic lateral sclerosis
P2860
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P2860
Non-native soluble oligomers of Cu/Zn superoxide dismutase (SOD1) contain a conformational epitope linked to cytotoxicity in amyotrophic lateral sclerosis (ALS).
description
article científic
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article scientifique
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articolo scientifico
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artigo científico
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bilimsel makale
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scientific article published on 02 April 2014
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vedecký článok
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vetenskaplig artikel
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videnskabelig artikel
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vědecký článek
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name
Non-native soluble oligomers o ...... ophic lateral sclerosis (ALS).
@en
Non-native soluble oligomers of Cu/Zn superoxide dismutase
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type
label
Non-native soluble oligomers o ...... ophic lateral sclerosis (ALS).
@en
Non-native soluble oligomers of Cu/Zn superoxide dismutase
@nl
prefLabel
Non-native soluble oligomers o ...... ophic lateral sclerosis (ALS).
@en
Non-native soluble oligomers of Cu/Zn superoxide dismutase
@nl
P2093
P2860
P356
P1433
P1476
Non-native soluble oligomers o ...... ophic lateral sclerosis (ALS).
@en
P2093
James M Fay
Lanette Fee
Michael Caplow
Rachel L Redler
P2860
P304
P356
10.1021/BI500158W
P407
P577
2014-04-02T00:00:00Z