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Coenzyme q10 therapyPharmacological Chaperones and Coenzyme Q10 Treatment Improves Mutant β-Glucocerebrosidase Activity and Mitochondrial Function in Neuronopathic Forms of Gaucher Disease.Screening of effective pharmacological treatments for MELAS syndrome using yeasts, fibroblasts and cybrid models of the diseaseClinical applications of coenzyme Q10.Emerging roles of apoptotic microtubules during the execution phase of apoptosis.Targeting autophagy and mitophagy for mitochondrial diseases treatment.AMPK As A Target in Rare Diseases.The Connections Among Autophagy, Inflammasome and Mitochondria.PEGylated versus non-PEGylated magnetic nanoparticles as camptothecin delivery system.Stabilization of apoptotic cells: generation of zombie cells.Apoptotic cells subjected to cold/warming exposure disorganize apoptotic microtubule network and undergo secondary necrosis.Coenzyme Q10 partially restores pathological alterations in a macrophage model of Gaucher disease.AMPK Regulation of Cell Growth, Apoptosis, Autophagy, and Bioenergetics.Apoptotic microtubules delimit an active caspase free area in the cellular cortex during the execution phase of apoptosis.Recovery of MERRF fibroblasts and cybrids pathophysiology by coenzyme Q10.Amitriptyline induces mitophagy that precedes apoptosis in human HepG2 cells.Mitochondrial Dysfunction in Lysosomal Storage Disorders.Mitochondrial Dynamics in Mitochondrial Diseases.Stabilization Of Apoptotic Cells: Generation Of Zombie Cells.Dynamic Reorganization of the Cytoskeleton during Apoptosis: The Two Coffins Hypothesis.Fluorinated Chaperone-β-Cyclodextrin Formulations for β-Glucocerebrosidase Activity Enhancement in Neuronopathic Gaucher Disease.Two coffins and a funeral: early or late caspase activation determines two types of apoptosis induced by DNA damaging agents.Critical role of AMP-activated protein kinase in the balance between mitophagy and mitochondrial biogenesis in MELAS disease.Targeted delivery of pharmacological chaperones for Gaucher disease to macrophages by a mannosylated cyclodextrin carrier.Intracellular cholesterol accumulation and coenzyme Q deficiency in Familial HypercholesterolemiaSecondary coenzyme Q10 deficiency triggers mitochondria degradation by mitophagy in MELAS fibroblastsPantothenate Rescues Iron Accumulation in Pantothenate Kinase-Associated Neurodegeneration Depending on the Type of MutationPathophysiological characterization of MERRF patient-specific induced neurons generated by direct reprogramming
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description
onderzoeker
@nl
researcher
@en
հետազոտող
@hy
name
Mario De la Mata
@ast
Mario De la Mata
@en
Mario De la Mata
@es
Mario De la Mata
@nl
type
label
Mario De la Mata
@ast
Mario De la Mata
@en
Mario De la Mata
@es
Mario De la Mata
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prefLabel
Mario De la Mata
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Mario De la Mata
@en
Mario De la Mata
@es
Mario De la Mata
@nl
P108
P106
P31
P496
0000-0003-1640-7887