Caroli disease
Caroli disease is a rare inherited disorder characterized by dilation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by ectasia. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal hypertension and congenital hepatic fibrosis. The differences between the causes of the two cases have not yet been discovered. Caroli disease is also associated with liver failure and polycystic kidney disease. The disease affects about 1 in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease.
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Caroli disease
Caroli disease is a rare inherited disorder characterized by dilation of the intrahepatic bile ducts. There are two types of Caroli disease, the most common being the simple, or isolated case where the bile ducts are widened by ectasia. The second, more complex, cause is commonly known as Caroli Syndrome. This complex form is also linked with portal hypertension and congenital hepatic fibrosis. The differences between the causes of the two cases have not yet been discovered. Caroli disease is also associated with liver failure and polycystic kidney disease. The disease affects about 1 in 1,000,000 people, with more reported cases of Caroli syndrome than of Caroli disease.
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Caroli disease is a rare inher ...... choledochal cyst derivatives.
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Choroba Carolego (ang. Caroli ...... wrotnego i marskości wątroby.
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Das Caroli-Syndrom, benannt na ...... als Caroli-Krankheit bekannt.
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La Enfermedad de Caroli es un ...... as de los quístes de colédoco.
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La maladie de Caroli est une a ...... le si elle s'avère nécessaire.
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La malattia di Caroli è una pa ...... sussistono altre alterazioni.
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Болезнь Кароли (синдром Кароли ...... ному типу, мутация гена PKHD1.
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737,259,314
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Figure 1 Biliary tract, system, or tree includes the gallbladder and the bile ducts.
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Caroli disease is a rare inher ...... ndrome than of Caroli disease.
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Choroba Carolego (ang. Caroli ...... wrotnego i marskości wątroby.
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Das Caroli-Syndrom, benannt na ...... als Caroli-Krankheit bekannt.
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La Enfermedad de Caroli es un ...... y fibrosis hepática congénita.
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La maladie de Caroli est une a ...... le si elle s'avère nécessaire.
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La malattia di Caroli è una pa ...... sussistono altre alterazioni.
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Болезнь Кароли (синдром Кароли ...... ному типу, мутация гена PKHD1.
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Caroli disease
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Caroli-Syndrom
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Choroba Carolego
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Enfermedad de Caroli
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Maladie de Caroli
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Malattia di Caroli
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Синдром Кароли
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Caroli disease
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