ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
about
Null mutations in LEPRE1 and CRTAP cause severe recessive osteogenesis imperfectaCardiopulmonary dysfunction in the Osteogenesis imperfecta mouse model Aga2 and human patients are caused by bone-independent mechanisms.Mechanisms and models of endoplasmic reticulum stress in chondrodysplasiaVitamin D and microRNAs in boneEndoplasmic reticulum stress in chondrodysplasias caused by mutations in collagen types II and XCole-Carpenter syndrome is caused by a heterozygous missense mutation in P4HBLethal skeletal dysplasia in mice and humans lacking the golgin GMAP-210E3 ubiquitin ligase synoviolin is involved in liver fibrogenesisEndoplasmic Reticulum Stress and Unfolded Protein Response in Cartilage Pathophysiology; Contributing Factors to Apoptosis and Osteoarthritis.Mutation in osteoactivin decreases bone formation in vivo and osteoblast differentiation in vitro.Targeted induction of endoplasmic reticulum stress induces cartilage pathology.Phenotype ontologies for mouse and man: bridging the semantic gap.Potential implications of cell therapy for osteogenesis imperfecta.eIF2α signaling regulates ischemic osteonecrosis through endoplasmic reticulum stressTranscriptional profiling of chondrodysplasia growth plate cartilage reveals adaptive ER-stress networks that allow survival but disrupt hypertrophyTargeting the LRP5 pathway improves bone properties in a mouse model of osteogenesis imperfecta.Taurine reduces ER stress in C. elegans.First mouse model for combined osteogenesis imperfecta and Ehlers-Danlos syndrome.Integration of multiple signaling regulates through apoptosis the differential osteogenic potential of neural crest-derived and mesoderm-derived OsteoblastsChaperoning osteogenesis: new protein-folding disease paradigms.Prevention of glucocorticoid induced-apoptosis of osteoblasts and osteocytes by protecting against endoplasmic reticulum (ER) stress in vitro and in vivo in female mice.HSP47 and FKBP65 cooperate in the synthesis of type I procollagen.New approaches to the representation and analysis of phenotype knowledge in human diseases and their animal modelsDeficient degradation of homotrimeric type I collagen, α1(I)3 glomerulopathy in oim mice.Molecular Consequences of the SERPINH1/HSP47 Mutation in the Dachshund Natural Model of Osteogenesis Imperfecta.Losartan ameliorates dystrophic epidermolysis bullosa and uncovers new disease mechanismsPorcine placenta hydrolysates regulate calcium disturbance in MC3T3-E1 osteoblastic cellsPorcine placenta hydrolysates enhance osteoblast differentiation through their antioxidant activity and effects on ER stress.New mouse models for metabolic bone diseases generated by genome-wide ENU mutagenesis.Thermally induced osteocyte damage initiates pro-osteoclastogenic gene expression in vivo.N-ethyl-N-nitrosourea mutagenesis produced a small number of mice with altered plasma electrolyte levelsThe unfolded protein response and its relevance to connective tissue diseases.Endoplasmic reticulum stress-unfolding protein response-apoptosis cascade causes chondrodysplasia in a col2a1 p.Gly1170Ser mutated mouse modelNew perspectives on osteogenesis imperfectaType I procollagen C-propeptide defects: study of genotype-phenotype correlation and predictive role of crystal structure.The unfolded protein response in skeletal development and homeostasis.The chaperone activity of 4PBA ameliorates the skeletal phenotype of Chihuahua, a zebrafish model for dominant osteogenesis imperfecta.17β-Estradiol inhibits ER stress-induced apoptosis through promotion of TFII-I-dependent Grp78 induction in osteoblasts.Involvement of endoplasmic reticulum stress in homocysteine-induced apoptosis of osteoblastic cells.Clinical Chemistry and Other Laboratory Tests on Mouse Plasma or Serum.
P2860
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P2860
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
description
2008 nî lūn-bûn
@nan
2008 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2008 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
name
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@ast
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en-gb
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@nl
type
label
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@ast
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en-gb
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@nl
altLabel
ER Stress-Mediated Apoptosis in a New Mouse Model of Osteogenesis imperfecta
@en
prefLabel
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@ast
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en-gb
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@nl
P2093
P2860
P50
P921
P3181
P1433
P1476
ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfecta
@en
P2093
Frank Thiele
Gabriele Hoelzlwimmer
Gerhard K H Przemeck
Helmut Fuchs
Koichiro Abe
Miep Helfrich
Stuart H Ralston
Thomas S Lisse
Wolfgang Hans
P2860
P3181
P356
10.1371/JOURNAL.PGEN.0040007
P407
P577
2008-02-01T00:00:00Z