Early alterations of brain cellular energy homeostasis in Huntington disease models
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Mouse models of polyglutamine diseases: review and data table. Part IPGC-1α, mitochondrial dysfunction, and Huntington's diseaseModeling Huntington's disease with induced pluripotent stem cellsPossible involvement of self-defense mechanisms in the preferential vulnerability of the striatum in Huntington's diseaseShaping the role of mitochondria in the pathogenesis of Huntington's diseaseRole of oxidative DNA damage in mitochondrial dysfunction and Huntington's disease pathogenesisHdhQ111 Mice Exhibit Tissue Specific Metabolite Profiles that Include Striatal Lipid AccumulationN-Acetylcysteine improves mitochondrial function and ameliorates behavioral deficits in the R6/1 mouse model of Huntington's diseaseMitochondrial dysfunction in neurodegenerative diseasesRegulation of neuronal bioenergy homeostasis by glutamateTriheptanoin improves brain energy metabolism in patients with Huntington diseaseA novel manganese-dependent ATM-p53 signaling pathway is selectively impaired in patient-based neuroprogenitor and murine striatal models of Huntington's diseaseEnhanced neuronal glucose transporter expression reveals metabolic choice in a HD Drosophila modelEnergy failure: does it contribute to neurodegeneration?Homeostatic adaptations in brain energy metabolism in mouse models of Huntington diseaseA broad phenotypic screen identifies novel phenotypes driven by a single mutant allele in Huntington's disease CAG knock-in mice.In vivo neurometabolic profiling in patients with spinocerebellar ataxia types 1, 2, 3, and 7Gender differences in the effect of tobacco use on brain phosphocreatine levels in methamphetamine-dependent subjectsPre-symptomatic activation of antioxidant responses and alterations in glucose and pyruvate metabolism in Niemann-Pick Type C1-deficient murine brainCompensation in Preclinical Huntington's Disease: Evidence From the Track-On HD StudyA dual role for AMP-activated protein kinase (AMPK) during neonatal hypoxic-ischaemic brain injury in miceCombinatorial assessments of brain tissue metabolomics and histopathology in rodent models of human immunodeficiency virus infectionMetabolism in HD: still a relevant mechanism?Inhibition of mitochondrial protein import by mutant huntingtinConditioned medium of human adipose-derived mesenchymal stem cells mediates protection in neurons following glutamate excitotoxicity by regulating energy metabolism and GAP-43 expressionOxygen consumption deficit in Huntington disease mouse brain under metabolic stressHuntington’s disease blood and brain show a common gene expression pattern and share an immune signature with Alzheimer’s diseaseEnergy dysfunction in Huntington's disease: insights from PGC-1α, AMPK, and CKB.AMP-activated protein kinase: new regulation, new roles?Genetic modifiers of Huntington's disease.Huntington's Disease: Pathogenic Mechanisms and Therapeutic Targets.Imaging and spectroscopic approaches to probe brain energy metabolism dysregulation in neurodegenerative diseases.AMPK in Neurodegenerative Diseases.Localized changes to glycogen synthase kinase-3 and collapsin response mediator protein-2 in the Huntington's disease affected brain.Triheptanoin for the treatment of brain energy deficit: A 14-year experience.Co-administration of creatine plus pyruvate prevents the effects of phenylalanine administration to female rats during pregnancy and lactation on enzymes activity of energy metabolism in cerebral cortex and hippocampus of the offspring.Early down-regulation of PKCδ as a pro-survival mechanism in Huntington's disease.Abnormal response to cortical activation in early stages of Huntington disease.A study of molecular changes relating to energy metabolism and cellular stress in people with Huntington's disease: looking for biomarkers.Oxidizing effects of exogenous stressors in Huntington's disease knock-in striatal cells--protective effect of cystamine and creatine.
P2860
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P2860
Early alterations of brain cellular energy homeostasis in Huntington disease models
description
2012 nî lūn-bûn
@nan
2012 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2012 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2012年の論文
@ja
2012年論文
@yue
2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
@wuu
name
Early alterations of brain cellular energy homeostasis in Huntington disease models
@ast
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en-gb
Early alterations of brain cellular energy homeostasis in Huntington disease models
@nl
type
label
Early alterations of brain cellular energy homeostasis in Huntington disease models
@ast
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en-gb
Early alterations of brain cellular energy homeostasis in Huntington disease models
@nl
prefLabel
Early alterations of brain cellular energy homeostasis in Huntington disease models
@ast
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en-gb
Early alterations of brain cellular energy homeostasis in Huntington disease models
@nl
P2093
P2860
P50
P921
P356
P1476
Early alterations of brain cellular energy homeostasis in Huntington disease models
@en
P2093
Fanny Mochel
Raphael Schiffmann
Sandrine Humbert
Vanessa C. Wheeler
Xingli Meng
P2860
P2880
P304
P356
10.1074/JBC.M111.309849
P407
P577
2012-01-06T00:00:00Z