Cholesterol accumulation sequesters Rab9 and disrupts late endosome function in NPC1-deficient cells
about
Niemann-Pick disease type CRab1a and Rab5a preferentially bind to binary lipid compositions with higher stored curvature elastic energyA syntaxin 10-SNARE complex distinguishes two distinct transport routes from endosomes to the trans-Golgi in human cellsPdro, a protein associated with late endosomes and lysosomes and implicated in cellular cholesterol homeostasisProteome-wide dysregulation by PRA1 depletion delineates a role of PRA1 in lipid transport and cell migrationDeficiency of niemann-pick type C-1 protein impairs release of human immunodeficiency virus type 1 and results in Gag accumulation in late endosomal/lysosomal compartmentsRab8-dependent recycling promotes endosomal cholesterol removal in normal and sphingolipidosis cellsRecycling Endosomes and Viral InfectionMolecular pathways for intracellular cholesterol accumulation: common pathogenic mechanisms in Niemann-Pick disease Type C and cystic fibrosisCholesterol balance in prion diseases and Alzheimer's diseaseRab13 Traffics on Vesicles Independent of Prenylation.Clues to neuro-degeneration in Niemann-Pick type C disease from global gene expression profilingARF6-mediated endosome recycling reverses lipid accumulation defects in Niemann-Pick Type C diseaseNiemann-Pick C1 functions independently of Niemann-Pick C2 in the initial stage of retrograde transport of membrane-impermeable lysosomal cargo.Inactivation of macrophage Rab7 by Burkholderia cenocepacia.The antiviral effector IFITM3 disrupts intracellular cholesterol homeostasis to block viral entry.Annexin A6-induced alterations in cholesterol transport and caveolin export from the Golgi complex.Sensitivity to lysosome-dependent cell death is directly regulated by lysosomal cholesterol contentA role for oxysterol-binding protein-related protein 5 in endosomal cholesterol trafficking.Alterations in gene expression in mutant amyloid precursor protein transgenic mice lacking Niemann-Pick type C1 proteinNiemann-Pick type C pathogenesis and treatment: from statins to sugars.Synaptojanin 1 is required for endolysosomal trafficking of synaptic proteins in cone photoreceptor inner segments.Proteasomal dysfunction and endoplasmic reticulum stress enhance trafficking of prion protein aggregates through the secretory pathway and increase accumulation of pathologic prion proteinRab proteins and the compartmentalization of the endosomal systemApolipoprotein E promotes β-amyloid trafficking and degradation by modulating microglial cholesterol levels.Cholesterol controls lipid endocytosis through Rab11.Cholinergic abnormalities, endosomal alterations and up-regulation of nerve growth factor signaling in Niemann-Pick type C disease.Prion infection impairs lysosomal degradation capacity by interfering with rab7 membrane attachment in neuronal cellsLipid signaling and the modulation of surface charge during phagocytosis.Development of a Rab9 transgenic mouse and its ability to increase the lifespan of a murine model of Niemann-Pick type C disease.Niemann-Pick type C disease proteins: orphan transporters or membrane rheostats?Adenovirus RIDα uncovers a novel pathway requiring ORP1L for lipid droplet formation independent of NPC1.Simvastatin treatment highlights a new role for the isoprenoid/cholesterol biosynthetic pathway in the modulation of emotional reactivity and cognitive performance in ratsSalmonella--the ultimate insider. Salmonella virulence factors that modulate intracellular survival.Regulation of cholesterol homeostasis.Insulin-Like Growth Factor-II/Cation-Independent Mannose 6-Phosphate Receptor in Neurodegenerative Diseases.Quantitative Co-Localization and Pattern Analysis of Endo-Lysosomal Cargo in Subcellular Image Cytometry and Validation on Synthetic Image Sets.Mechanisms and functions of lysosome positioning.Routes and mechanisms of post-endosomal cholesterol trafficking: A story that never ends.Regulation of late endosomal/lysosomal maturation and trafficking by cortactin affects Golgi morphology.
P2860
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P2860
Cholesterol accumulation sequesters Rab9 and disrupts late endosome function in NPC1-deficient cells
description
2006 nî lūn-bûn
@nan
2006 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@ast
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@en
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@nl
type
label
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@ast
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@en
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@nl
prefLabel
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@ast
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@en
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@nl
P2860
P356
P1476
Cholesterol accumulation seque ...... nction in NPC1-deficient cells
@en
P2093
Suzanne R Pfeffer
P2860
P304
P356
10.1074/JBC.M601679200
P407
P577
2006-06-30T00:00:00Z