Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
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AAV.Dysferlin Overlap Vectors Restore Function in Dysferlinopathy Animal ModelsTriadopathies: an emerging class of skeletal muscle diseases.The absence of dysferlin induces the expression of functional connexin-based hemichannels in human myotubesPlasma Membrane Repair: A Central Process for Maintaining Cellular Homeostasis.Identification of Small Ankyrin 1 as a Novel Sarco(endo)plasmic Reticulum Ca2+-ATPase 1 (SERCA1) Regulatory Protein in Skeletal Muscle.Intermittent Glucocorticoid Dosing Improves Muscle Repair and Function in Mice with Limb Girdle Muscular Dystrophy.Systemic Delivery of Dysferlin Overlap Vectors Provides Long-Term Gene Expression and Functional Improvement for Dysferlinopathy.Mining for mitochondrial mechanisms: linking known syndromes to mitochondrial function.Coupling of excitation to Ca2+ release is modulated by dysferlin.A novel dysferlin mutant pseudoexon bypassed with antisense oligonucleotides.Dysferlin Binds SNAREs (Soluble N-Ethylmaleimide-sensitive Factor (NSF) Attachment Protein Receptors) and Stimulates Membrane Fusion in a Calcium-sensitive Manner.DNA Microarray Analysis on the Genes Differentially Expressed in the Liver of the Pufferfish, Takifugu rubripes, Following an Intramuscular Administration of TetrodotoxinAre mechanically sensitive regulators involved in the function and (patho)physiology of cerebral palsy-related contractures?Serum exosomes can restore cellular function in vitro and be used for diagnosis in dysferlinopathy.Tamoxifen prolongs survival and alleviates symptoms in mice with fatal X-linked myotubular myopathy
P2860
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P2860
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
description
2014 nî lūn-bûn
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2014 թուականին հրատարակուած գիտական յօդուած
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2014 թվականին հրատարակված գիտական հոդված
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2014年の論文
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2014年論文
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2014年論文
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2014年論文
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2014年論文
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2014年論文
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2014年论文
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name
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@ast
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@en
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@nl
type
label
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@ast
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@en
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@nl
prefLabel
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@ast
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@en
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@nl
P2093
P2860
P3181
P356
P1476
Dysferlin at transverse tubules regulates Ca(2+) homeostasis in skeletal muscle
@en
P2093
Christopher W. Ward
Jaclyn P. Kerr
Robert J. Bloch
P2860
P3181
P356
10.3389/FPHYS.2014.00089
P407
P577
2014-01-01T00:00:00Z