Nebulette: a 107 kD nebulin-like protein in cardiac muscle
about
Functional dissection of nebulette demonstrates actin binding of nebulin-like repeats and Z-line targeting of SH3 and linker domainsMyopalladin, a novel 145-kilodalton sarcomeric protein with multiple roles in Z-disc and I-band protein assembliesNebulette mutations are associated with dilated cardiomyopathy and endocardial fibroelastosisArgBP2, a multiple Src homology 3 domain-containing, Arg/Abl-interacting protein, is phosphorylated in v-Abl-transformed cells and localized in stress fibers and cardiocyte Z-disksMutations in the nebulin gene associated with autosomal recessive nemaline myopathyLasp-1, a novel type of actin-binding protein accumulating in cell membrane extensionsNebulin-deficient mice exhibit shorter thin filament lengths and reduced contractile function in skeletal muscleDifferentiation- and stress-dependent nuclear cytoplasmic redistribution of myopodin, a novel actin-bundling proteinPhenobarbital mediates an epigenetic switch at the constitutive androstane receptor (CAR) target gene Cyp2b10 in the liver of B6C3F1 miceZyxin interacts with the SH3 domains of the cytoskeletal proteins LIM-nebulette and Lasp-1The vertebrate muscle Z-disc: sarcomere anchor for structure and signallingThe Nebulin family: an actin support groupTropomodulin isoforms regulate thin filament pointed-end capping and skeletal muscle physiologyA nebulin ruler does not dictate thin filament lengthsTargeted disruption of the Lasp-1 gene is linked to increases in histamine-stimulated gastric HCl secretionMyofibril assembly visualized by imaging N-RAP, alpha-actinin, and actin in living cardiomyocytes.Investigating lasp-2 in cell adhesion: new binding partners and roles in motility.Nebulette is a powerful cytolinker organizing desmin and actin in mouse heartsLASP2 suppresses colorectal cancer progression through JNK/p38 MAPK pathway meditated epithelial-mesenchymal transition.Nonmuscle myosin IIB, a sarcomeric component in the extraocular muscles.Actin-titin interaction in cardiac myofibrils: probing a physiological role.Neutral sphingomyelinase-3 mediates TNF-stimulated oxidant activity in skeletal muscleDynamic regulation of sarcomeric actin filaments in striated muscleFishing out proteins that bind to titinNebulin, a major player in muscle health and diseaseTNF/TNFR1 signaling mediates doxorubicin-induced diaphragm weakness.Postnatal changes in the developing rat extraocular musclesThe sarcomeric protein nebulin: another multifunctional giant in charge of muscle strength optimizationI-band titin in cardiac muscle is a three-element molecular spring and is critical for maintaining thin filament structureNebulin regulates the assembly and lengths of the thin filaments in striated muscleUse of thin filament reconstituted muscle fibres to probe the mechanism of force generation.Exome Sequencing Identifies Pathogenic and Modifier Mutations in a Child With Sporadic Dilated Cardiomyopathy.Mutations in NEBL encoding the cardiac Z-disk protein nebulette are associated with various cardiomyopathies.Assembly and maintenance of the sarcomere night and day.Ectopic expression of LIM-nebulette (LASP2) reveals roles in cell migration and spreading.Thin filament length regulation in striated muscle sarcomeres: pointed-end dynamics go beyond a nebulin ruler.Lifting the nebula: novel insights into skeletal muscle contractility.The interactome of LIM domain proteins: the contributions of LIM domain proteins to heart failure and heart development.A two-segment model for thin filament architecture in skeletal muscle.Myofibrillar Z-discs Are a Protein Phosphorylation Hot Spot with Protein Kinase C (PKCα) Modulating Protein Dynamics.
P2860
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P2860
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
description
1995 nî lūn-bûn
@nan
1995 թուականին հրատարակուած գիտական յօդուած
@hyw
1995 թվականին հրատարակված գիտական հոդված
@hy
1995年の論文
@ja
1995年論文
@yue
1995年論文
@zh-hant
1995年論文
@zh-hk
1995年論文
@zh-mo
1995年論文
@zh-tw
1995年论文
@wuu
name
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@ast
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@en
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@nl
type
label
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@ast
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@en
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@nl
prefLabel
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@ast
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@en
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@nl
P3181
P356
P1433
P1476
Nebulette: a 107 kD nebulin-like protein in cardiac muscle
@en
P2093
P304
P3181
P356
10.1002/CM.970320305
P407
P577
1995-01-01T00:00:00Z