Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
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Update in Cystic Fibrosis 2014Molecular mechanism of pancreatic and salivary gland fluid and HCO3 secretionMolecular basis for pH-dependent mucosal dehydration in cystic fibrosis airwaysAirway Gland Structure and FunctionAirway hydration and COPDEssential role of carbonic anhydrase XII in secretory gland fluid and HCO3 (-) secretion revealed by disease causing human mutationCharacterizing Lung Disease in Cystic Fibrosis with Magnetic Resonance Imaging and Airway Physiology.Impact of CFTR Modulation on Intestinal pH, Motility, and Clinical Outcomes in Patients With Cystic Fibrosis and the G551D Mutation.Neonates with cystic fibrosis have a reduced nasal liquid pH; a small pilot study.Native small airways secrete bicarbonate.Mimicking the host and its microenvironment in vitro for studying mucosal infections by Pseudomonas aeruginosa.Use of kinase inhibitors to correct ΔF508-CFTR function.State of progress in treating cystic fibrosis respiratory disease.A functional anatomic defect of the cystic fibrosis airway.Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosisHuman cystic fibrosis airway epithelia have reduced Cl- conductance but not increased Na+ conductance.Biogeochemical forces shape the composition and physiology of polymicrobial communities in the cystic fibrosis lung.Multidimensional clinical phenotyping of an adult cystic fibrosis patient populationRNA Interference Screen to Identify Kinases That Suppress Rescue of ΔF508-CFTR.ENaC in the Rabbit Lacrimal Gland and its Changes During Sjögren Syndrome and Pregnancy.Calcium-sensing receptor stimulates Cl(-)- and SCFA-dependent but inhibits cAMP-dependent HCO3(-) secretion in colon.Cystic Fibrosis Gene Therapy in the UK and Elsewhere.Recent advances in understanding and managing cystic fibrosis transmembrane conductance regulator dysfunction.Cystic fibrosis: an inherited disease affecting mucin-producing organs.Forkhead transcription factor FoxA1 regulates sweat secretion through Bestrophin 2 anion channel and Na-K-Cl cotransporter 1Nanoparticles that deliver triplex-forming peptide nucleic acid molecules correct F508del CFTR in airway epitheliumReduced airway surface pH impairs bacterial killing in the porcine cystic fibrosis lung.A large-scale quantitative EM study on activation of olfactory glands shows no effect of cholinergic agents.CFTR, mucins, and mucus obstruction in cystic fibrosis.Transepithelial bicarbonate secretion: lessons from the pancreasDynamic modulation of ANO1/TMEM16A HCO3(-) permeability by Ca2+/calmodulin.Mucociliary transport in porcine trachea: differential effects of inhibiting chloride and bicarbonate secretion.Combination therapy with cystic fibrosis transmembrane conductance regulator modulators augment the airway functional microanatomy.Regulated mucin secretion from airway epithelial cellsClinical insights from metagenomic analysis of sputum samples from patients with cystic fibrosis.Defective postsecretory maturation of MUC5B mucin in cystic fibrosis airwaysSupramolecular dynamics of mucus.Expert opinion in biological therapy: update on developments in lung gene transfer.Disease-modifying genes and monogenic disorders: experience in cystic fibrosis.Importance of bicarbonate transport in pH control during amelogenesis - need for functional studies.
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Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
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2010 nî lūn-bûn
@nan
2010 թուականի Դեկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի դեկտեմբերին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@ast
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@en
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@nl
type
label
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@ast
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@en
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@nl
prefLabel
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@ast
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@en
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@nl
P2860
P3181
P1476
Role of epithelial HCO3⁻ transport in mucin secretion: lessons from cystic fibrosis
@en
P2093
Paul M Quinton
P2860
P304
P3181
P356
10.1152/AJPCELL.00362.2010
P407
P577
2010-12-01T00:00:00Z