β-Catenin is central to DUX4-driven network rewiring in facioscapulohumeral muscular dystrophy.
about
DUX4 induces a transcriptome more characteristic of a less-differentiated cell state and inhibits myogenesisRet function in muscle stem cells points to tyrosine kinase inhibitor therapy for facioscapulohumeral muscular dystrophy.A Human Pluripotent Stem Cell Model of Facioscapulohumeral Muscular Dystrophy-Affected Skeletal Muscles.Model systems of DUX4 expression recapitulate the transcriptional profile of FSHD cells.Activation of the wnt/β-Catenin Signaling Pathway in Polymyositis, Dermatomyositis and Duchenne Muscular DystrophyPAX7 target genes are globally repressed in facioscapulohumeral muscular dystrophy skeletal muscle.Overexpression of the double homeodomain protein DUX4c interferes with myofibrillogenesis and induces clustering of myonuclei.Functional domains of the FSHD-associated DUX4 protein.Tissue-specific activities of the Fat1 cadherin cooperate to control neuromuscular morphogenesis.
P2860
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P2860
β-Catenin is central to DUX4-driven network rewiring in facioscapulohumeral muscular dystrophy.
description
2015 nî lūn-bûn
@nan
2015 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2015 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2015年の論文
@ja
2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
@wuu
name
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@ast
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@en
type
label
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@ast
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@en
prefLabel
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@ast
β-Catenin is central to DUX4-d ...... ulohumeral muscular dystrophy.
@en
P2093
P2860
P50
P356
P1476
β-Catenin is central to DUX4-d ...... pulohumeral muscular dystrophy
@en
P2093
Andrew E Teschendorff
Christopher R S Banerji
Richard W Orrell
Simone Severini
P2860
P304
P356
10.1098/RSIF.2014.0797
P577
2015-01-01T00:00:00Z