Murine cathepsin F deficiency causes neuronal lipofuscinosis and late-onset neurological disease.
about
The novel neuronal ceroid lipofuscinosis gene MFSD8 encodes a putative lysosomal transporterCathepsin F mutations cause Type B Kufs disease, an adult-onset neuronal ceroid lipofuscinosisLysosomal function in macromolecular homeostasis and bioenergetics in Parkinson's disease.Predominance of interferon-related responses in the brain during murine malaria, as identified by microarray analysis.Cysteine proteases: destruction ability versus immunomodulation capacity in immune cells.Cysteine cathepsin S as an immunomodulatory target: present and future trends.Cathepsin D expression level affects alpha-synuclein processing, aggregation, and toxicity in vivo.Role of Cathepsins in Mycobacterium tuberculosis Survival in Human Macrophages.Neuronal ceroid lipofuscinosis type CLN2: a new rationale for the construction of phenotypic subgroups based on a survey of 25 cases in South America.Sexual dimorphism in the mast cell transcriptome and the pathophysiological responses to immunological and psychological stress.Lysosomes as "suicide bags" in cell death: myth or reality?Alu-Derived Alternative Splicing Events Specific to Macaca Lineages in CTSF Gene.Cysteine cathepsins in neurological disorders.Inherited diseases caused by mutations in cathepsin protease genes.NCLs and ER: A stressful relationship.Enhanced detection method for corneal protein identification using shotgun proteomics.A novel role of the Batten disease gene CLN3: association with BMP synthesis.Proliferative and nonproliferative lesions of the rat and mouse central and peripheral nervous systems.An alternative splicing variant in Clcn7-/- mice prevents osteopetrosis but not neural and retinal degeneration.Active Site Mapping of Human Cathepsin F with Dipeptide Nitrile Inhibitors.Increased Immunoreactivity of Cathepsins in the Rat Esophagus under Chronic Acid Reflux Esophagitis
P2860
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P2860
Murine cathepsin F deficiency causes neuronal lipofuscinosis and late-onset neurological disease.
description
2006 nî lūn-bûn
@nan
2006 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2006 թվականի մարտին հրատարակված գիտական հոդված
@hy
2006年の論文
@ja
2006年論文
@yue
2006年論文
@zh-hant
2006年論文
@zh-hk
2006年論文
@zh-mo
2006年論文
@zh-tw
2006年论文
@wuu
name
Murine cathepsin F deficiency ...... te-onset neurological disease.
@ast
Murine cathepsin F deficiency ...... te-onset neurological disease.
@en
type
label
Murine cathepsin F deficiency ...... te-onset neurological disease.
@ast
Murine cathepsin F deficiency ...... te-onset neurological disease.
@en
prefLabel
Murine cathepsin F deficiency ...... te-onset neurological disease.
@ast
Murine cathepsin F deficiency ...... te-onset neurological disease.
@en
P2093
P2860
P1476
Murine cathepsin F deficiency ...... te-onset neurological disease.
@en
P2093
Chi-Hui Tang
Harold A Chapman
Je-Wook Lee
Liliane Robillard
Michael G Galvez
P2860
P304
P356
10.1128/MCB.26.6.2309-2316.2006
P407
P50
P577
2006-03-01T00:00:00Z