Cardiac involvement in patients with muscular dystrophies: magnetic resonance imaging phenotype and genotypic considerations.
about
Multi-parametric MRI at 14T for muscular dystrophy mice treated with AAV vector-mediated gene therapyMesodermal iPSC-derived progenitor cells functionally regenerate cardiac and skeletal muscleGadolinium-enhanced cardiovascular magnetic resonance: administered dose in relationship to United States Food and Drug Administration (FDA) guidelines.Left ventricular systolic function and the pattern of late-gadolinium-enhancement independently and additively predict adverse cardiac events in muscular dystrophy patientsEplerenone for early cardiomyopathy in Duchenne muscular dystrophy: a randomised, double-blind, placebo-controlled trialCardiovascular magnetic resonance of cardiomyopathy in limb girdle muscular dystrophy 2B and 2IMyocardial fibrosis in patients with myotonic dystrophy type 1: a cardiovascular magnetic resonance studyAquapuncture Using Stem Cell Therapy to Treat Mdx Mice.Investigation of cardiomyopathy using cardiac magnetic resonance imaging part 2: Rare phenotypes.Sustaining cardiac claudin-5 levels prevents functional hallmarks of cardiomyopathy in a muscular dystrophy mouse model.Structural and functional cardiac changes in myotonic dystrophy type 1: a cardiovascular magnetic resonance studyCardiomyopathy in the dystrophin/utrophin-deficient mouse model of severe muscular dystrophy is characterized by dysregulation of matrix metalloproteinases.The Angiotensin Converting Enzyme Inhibitor Lisinopril Improves Muscle Histopathology but not Contractile Function in a Mouse Model of Duchenne Muscular Dystrophy.Identification of cardiomyopathy associated circulating miRNA biomarkers in patients with muscular dystrophy using a complementary cardiovascular magnetic resonance and plasma profiling approachSevere dilated cardiomyopathy in a patient with myotonic dystrophy type 2 and homozygous repeat expansion in ZNF9.Impact of cardiovascular magnetic resonance on management and clinical decision-making in heart failure patients.Myocardial Contractile Dysfunction Is Present without Histopathology in a Mouse Model of Limb-Girdle Muscular Dystrophy-2F and Is Prevented after Claudin-5 Virotherapy.Evolving diagnostic and prognostic imaging of the various cardiomyopathies.Neuromuscular disorders in zebrafish: state of the art and future perspectives.Interleukin 1 Receptor-Like 1 Protein (ST2) is a Potential Biomarker for Cardiomyopathy in Duchenne Muscular Dystrophy.Transverse tubule remodelling: a cellular pathology driven by both sides of the plasmalemma?Prenatal diagnosis of congenital myopathies and muscular dystrophies.Striated muscle function, regeneration, and repairSymptomatic Trifascicular Block in Steinert's Disease: Is It Too Soon for a Pacemaker?Myotonic Dystrophy Type 1 Management and Therapeutics.Can Human Pluripotent Stem Cell-Derived Cardiomyocytes Advance Understanding of Muscular Dystrophies?Cardiac Involvement Classification and Therapeutic Management in Patients with Duchenne Muscular Dystrophy.Magnetic resonance imaging of myocardial strain: A review of current approaches.Magnetic resonance of the heart in a muscular dystrophy patient with an MR conditional ICD: assessment of safety, diagnostic value and technical limitationsProgression of Duchenne Cardiomyopathy Presenting with Chest Pain and Troponin Elevation.Epicardial ablation of ventricular tachycardia in a patient with Becker muscular dystrophy.Long-term miR-669a therapy alleviates chronic dilated cardiomyopathy in dystrophic mice.Early treatment with lisinopril and spironolactone preserves cardiac and skeletal muscle in Duchenne muscular dystrophy mice.MicroRNA based treatment of cardiomyopathy: not all dystrophies are created equal.Early myocardial damage assessment in dystrophinopathies using (99)Tc(m)-MIBI gated myocardial perfusion imaging.Proteomic profiling of cardiomyopathic tissue from the aged mdx model of Duchenne muscular dystrophy reveals a drastic decrease in laminin, nidogen and annexin.Subepicardial dysfunction leads to global left ventricular systolic impairment in patients with limb girdle muscular dystrophy 2I.The role of βII spectrin in cardiac health and disease.Photobiomodulation therapy protects skeletal muscle and improves muscular function of mdx mice in a dose-dependent manner through modulation of dystrophin.Myocardial Fibrosis and Left Ventricular Dysfunction in Duchenne Muscular Dystrophy Carriers Using Cardiac Magnetic Resonance Imaging.
P2860
Q27308877-73B11765-B649-4197-A730-3A3B2C28ADA3Q27331430-D0027A40-878F-4960-9693-D2DD6D287E9FQ34178860-2B4D4CBA-D2E4-480B-B827-B553801E85AEQ34250674-BE479394-B31C-4696-9355-7172B1C2096FQ35181260-12E9AC9A-DFD8-421E-8142-87C02486C07AQ35206123-D094377E-5E46-449C-B05B-3C68E95F1AD2Q35576188-D6B7E2DD-4B77-4B32-A848-8FA4FFA36E33Q35649642-54C37290-6089-4C56-AD7C-A73897585937Q35999436-D25E313E-DFAA-4124-BA0F-C4E2A04DE35EQ36085348-737AB5BB-9485-42BB-A56E-30F59F8CA801Q36288840-0B8DE583-E29F-474D-B8A7-1585514030FEQ36356925-59E049A5-4FD6-4E74-9BF2-75356FFF15E9Q36817631-0CE615EF-ED4B-4421-BCC8-550070BAA084Q36875975-37FCD738-84B3-48E0-B6E3-B104C26F2D28Q36918560-3F20DE6B-1F60-48E1-89E2-086C652E6A07Q37364419-ACB760E6-747B-43F0-B50E-E9E78D8A3052Q37474934-3A8D2D43-FDAA-4671-9A71-5F2C9FCAA310Q38006744-31E59D83-BF15-4E47-90C8-D03D49396C62Q38098929-B1F9BCEC-AFBF-4C7B-92BF-614746555C59Q38640186-B7C71357-DE06-42D6-A3F0-6D8286330634Q38684811-07E5E3CF-B21D-4F62-865E-B82C825A75B7Q38838661-2AE1770B-5E92-4947-B780-6AF14962F41AQ38857890-DE32643F-96BD-47A1-BBA8-181F4AF51EBCQ38955528-94683447-B1E6-4AB2-BB72-7730A689CF03Q39003493-BBFB76D1-40D4-4E46-8D66-81C004149273Q39010745-4B0C21EE-F9D7-42C9-9CB4-5C84BE0ABF5EQ39166732-9FD7DFB2-3466-4979-9A4D-92C3CC32D8D1Q39283262-5CF10BA2-DED4-49E4-9DB6-43B7B78AB4FEQ39403652-38BCC547-6E09-436D-94B0-CE1DD82BB5EBQ41922953-7D381BFB-0446-4F5E-AAB7-DBCD1400F2E5Q42071610-F84195A0-122B-4193-8CF7-22BDE8AA3082Q42275401-D523EDA6-F47E-4619-80E7-346AFF8B75EBQ42855263-0D7B9D2D-921E-45B1-A623-F59CE6437788Q42906190-65BE00D9-7A44-4D01-9204-B8D1DE51360EQ43131882-1A211A0F-2557-4175-8826-8DF8DCA7AB12Q44232941-DF794527-D423-471C-BA7C-B8877C6E9C00Q45384428-7EF78184-4027-4345-A83B-9AA4220116BAQ46263328-F9CE24FF-2684-495F-9BA6-4B3F4AD1C602Q47325217-25C33340-B651-4F41-AD3E-DC264A526DCFQ48669653-83F64DCB-1C73-4E08-B1E7-85FFF483A031
P2860
Cardiac involvement in patients with muscular dystrophies: magnetic resonance imaging phenotype and genotypic considerations.
description
2011 nî lūn-bûn
@nan
2011 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Cardiac involvement in patient ...... and genotypic considerations.
@ast
Cardiac involvement in patient ...... and genotypic considerations.
@en
type
label
Cardiac involvement in patient ...... and genotypic considerations.
@ast
Cardiac involvement in patient ...... and genotypic considerations.
@en
prefLabel
Cardiac involvement in patient ...... and genotypic considerations.
@ast
Cardiac involvement in patient ...... and genotypic considerations.
@en
P2093
P2860
P1476
Cardiac involvement in patient ...... and genotypic considerations.
@en
P2093
David Verhaert
Jill A Rafael-Fortney
Kathryn Richards
Subha V Raman
P2860
P356
10.1161/CIRCIMAGING.110.960740
P577
2011-01-01T00:00:00Z