Dyclonine rescues frataxin deficiency in animal models and buccal cells of patients with Friedreich's ataxia.
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Epigenetics and Triplet-Repeat Neurological DiseasesEmerging functional cross-talk between the Keap1-Nrf2 system and mitochondriaActivating frataxin expression by repeat-targeted nucleic acidsLymphoblast Oxidative Stress Genes as Potential Biomarkers of Disease Severity and Drug Effect in Friedreich's AtaxiaA novel GAA-repeat-expansion-based mouse model of Friedreich's ataxiaStable isotopes and LC-MS for monitoring metabolic disturbances in Friedreich's ataxia platelets.Reversal of epigenetic promoter silencing in Friedreich ataxia by a class I histone deacetylase inhibitor.Translating HDAC inhibitors in Friedreich's ataxia.Pharmacological therapeutics in Friedreich ataxia: the present state.Overexpression of Drosophila frataxin triggers cell death in an iron-dependent manner.Early VGLUT1-specific parallel fiber synaptic deficits and dysregulated cerebellar circuit in the KIKO mouse model of Friedreich ataxia.Activation of Frataxin Protein Expression by Antisense Oligonucleotides Targeting the Mutant Expanded Repeat.Phenothiazine antioxidants increase mitochondrial biogenesis and frataxin levels in Friedreich's ataxia cellsEmerging Regulatory Role of Nrf2 in Iron, Heme, and Hemoglobin Metabolism in Physiology and Disease
P2860
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P2860
Dyclonine rescues frataxin deficiency in animal models and buccal cells of patients with Friedreich's ataxia.
description
2014 nî lūn-bûn
@nan
2014 թուականի Օգոստոսին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի օգոստոսին հրատարակված գիտական հոդված
@hy
2014年の論文
@ja
2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@ast
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@en
type
label
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@ast
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@en
prefLabel
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@ast
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@en
P2093
P2860
P356
P1476
Dyclonine rescues frataxin def ...... ents with Friedreich's ataxia.
@en
P2093
Brandon Brown
Brian D Scott
Gino A Cortopassi
Heike Wulff
Marissa Z McMackin
Mark A Pook
Mittal Jasoliya
Sunil Sahdeo
Susan L Perlman
P2860
P304
P356
10.1093/HMG/DDU408
P577
2014-08-11T00:00:00Z