Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy. - Wikidata - thesis-toulmin - TriplyDB

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

http://www.wikidata.org/entity/Q34631169

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Peroxisomes in brain development and function Redox interplay between mitochondria and peroxisomes Protective Effects of α-Tocopherol, γ-Tocopherol and Oleic Acid, Three Compounds of Olive Oils, and No Effect of Trolox, on 7-Ketocholesterol-Induced Mitochondrial and Peroxisomal Dysfunction in Microglial BV-2 Cells Functional Characterization of IPSC-Derived Brain Cells as a Model for X-Linked Adrenoleukodystrophy X-linked adrenoleukodystrophy (X-ALD): clinical presentation and guidelines for diagnosis, follow-up and management.Improvement of the Rett syndrome phenotype in a MeCP2 mouse model upon treatment with levodopa and a dopa-decarboxylase inhibitor An under-recognised cause of spastic paraparesis in middle-aged women Pathophysiology of X-linked adrenoleukodystrophy.Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy.Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.The difficulty in diagnosing X linked adrenoleucodystrophy and the importance of identifying cerebral involvement.Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy Endocrine manifestations related to inherited metabolic diseases in adults.Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy Partial rescue of Rett syndrome by ω-3 polyunsaturated fatty acids (PUFAs) oil Activation of sirtuin 1 as therapy for the peroxisomal disease adrenoleukodystrophy.Oxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophy Glutathione imbalance in patients with X-linked adrenoleukodystrophy 25-hydroxycholesterol contributes to cerebral inflammation of X-linked adrenoleukodystrophy through activation of the NLRP3 inflammasome.Systemic Radical Scavenger Treatment of a Mouse Model of Rett Syndrome: Merits and Limitations of the Vitamin E Derivative Trolox Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.Mitochondrial sirtuins--a new therapeutic target for repair and protection in multiple sclerosis.Advances and pitfalls of cell therapy in metabolic leukodystrophies.Wallerian degeneration: an emerging axon death pathway linking injury and disease.Mitochondrial dysfunction in central nervous system white matter disorders.Oxidative Stress in Patients with X-Linked Adrenoleukodystrophy.Adrenoleukodystrophy - neuroendocrine pathogenesis and redefinition of natural history.Mechanisms of Antioxidant Induction with High-Dose N-Acetylcysteine in Childhood Cerebral Adrenoleukodystrophy.Evidence of Oxidative Stress and Secondary Mitochondrial Dysfunction in Metabolic and Non-Metabolic Disorders.Peroxisome deficiency but not the defect in ether lipid synthesis causes activation of the innate immune system and axonal loss in the central nervous system Treatment effect of coenzyme Q(10) and an antioxidant cocktail in fibroblasts of patients with Sanfilippo disease.Sisyphus in Neverland.Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus-Merzbacher disease.Functional characterization of novel genotypes and cellular oxidative stress studies in propionic acidemia.Therapeutic strategies in adrenoleukodystrophy.Impaired mitochondrial oxidative phosphorylation in the peroxisomal disease X-linked adrenoleukodystrophy.Leukodystrophy: Basic and Clinical.Altered Redox Homeostasis in Branched-Chain Amino Acid Disorders, Organic Acidurias, and Homocystinuria.

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Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

http://www.wikidata.org/entity/Q34631169

description

2011 nî lūn-bûn

@nan

2011 թուականի Յուլիսին հրատարակուած գիտական յօդուած

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2011 թվականի հուլիսին հրատարակված գիտական հոդված

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2011年の論文

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2011年論文

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2011年論文

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2011年論文

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2011年論文

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2011年論文

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2011年论文

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name

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@ast

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@en

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@nl

type

label

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@ast

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@en

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@nl

prefLabel

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@ast

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@en

Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.

@nl

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Annals of Neurology

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Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy

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Isidre Ferrer

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Jone López-Erauskin

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Jorge Galino

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Manuel Portero-Otin

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P2860

The human peroxisomal ABC half transporter ALDP functions as a homodimer and accepts acyl-CoA esters

The ABC transporter proteins Pat1 and Pat2 are required for import of long-chain fatty acids into peroxisomes of Saccharomyces cerevisiae

Mitochondrial dysfunction and oxidative stress in neurodegenerative diseases

Beneficial effects of creatine, CoQ10, and lipoic acid in mitochondrial disorders

Axonal and neuronal degeneration in multiple sclerosis: mechanisms and functional consequences.

Diabetic beta-cells can achieve self-protection against oxidative stress through an adaptive up-regulation of their antioxidant defenses.

Adrenomyeloneuropathy: a neuropathologic review featuring its noninflammatory myelopathy.

Mechanism of toxicity in rotenone models of Parkinson's disease.

Feeding acetyl-L-carnitine and lipoic acid to old rats significantly improves metabolic function while decreasing oxidative stress.

Oral treatment with alpha-lipoic acid improves symptomatic diabetic polyneuropathy: the SYDNEY 2 trial.

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10.1002/ANA.22363

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1

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70

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Reinald Pamplona

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Stéphane Fourcade

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3229843

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