Mitochondrial Diseases Part I: mouse models of OXPHOS deficiencies caused by defects in respiratory complex subunits or assembly factors.
about
Dynamics of Human Mitochondrial Complex I Assembly: Implications for Neurodegenerative DiseasesDysfunctional mitochondrial bioenergetics and the pathogenesis of hepatic disordersUPR(mt)-mediated cytoprotection and organismal aging.The genetics and pathology of mitochondrial disease.Review: Central nervous system involvement in mitochondrial diseaseMouse models for mitochondrial diseases.The Peroxisome-Mitochondria Connection: How and Why?microRNA-4331 Promotes Transmissible Gastroenteritis Virus (TGEV)-induced Mitochondrial Damage Via Targeting RB1, Upregulating Interleukin-1 Receptor Accessory Protein (IL1RAP), and Activating p38 MAPK Pathway In Vitro.Knockout of Tmem70 alters biogenesis of ATP synthase and leads to embryonal lethality in mice.Nutritional Interventions for Mitochondrial OXPHOS Deficiencies: Mechanisms and Model Systems.Loss of Pink1 modulates synaptic mitochondrial bioenergetics in the rat striatum prior to motor symptoms: concomitant complex I respiratory defects and increased complex II-mediated respiration.The emerging role of immune dysfunction in mitochondrial diseases as a paradigm for understanding immunometabolism.A disease-associated Aifm1 variant induces severe myopathy in knockin mice.
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P2860
Mitochondrial Diseases Part I: mouse models of OXPHOS deficiencies caused by defects in respiratory complex subunits or assembly factors.
description
2015 nî lūn-bûn
@nan
2015 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2015 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2015年の論文
@ja
2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
@wuu
name
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@ast
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@en
type
label
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@ast
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@en
prefLabel
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@ast
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@en
P2093
P2860
P1433
P1476
Mitochondrial Diseases Part I: ...... subunits or assembly factors.
@en
P2093
Alessandra Torraco
Francisca Diaz
Susana Peralta
P2860
P356
10.1016/J.MITO.2015.01.009
P577
2015-02-04T00:00:00Z