Molecular and functional defects in kidneys of mice lacking collagen alpha 3(IV): implications for Alport syndrome.
about
Agrin is a major heparan sulfate proteoglycan in the human glomerular basement membraneDevelopmental and pathogenic mechanisms of basement membrane assemblyPhysiological levels of tumstatin, a fragment of collagen IV alpha3 chain, are generated by MMP-9 proteolysis and suppress angiogenesis via alphaV beta3 integrinIn vivo expression of putative LMX1B targets in nail-patella syndrome kidneysStage-specific action of matrix metalloproteinases influences progressive hereditary kidney disease.Crystal structure of NC1 domains. Structural basis for type IV collagen assembly in basement membranesInsight into podocyte differentiation from the study of human genetic disease: nail-patella syndrome and transcriptional regulation in podocytesUpdate on the glomerular filtration barrierDisruption of Myosin 1e promotes podocyte injuryLarge-scale identification of genes implicated in kidney glomerulus development and function.Distribution and function of laminins in the neuromuscular system of developing, adult, and mutant miceThe extracellular matrix in development and morphogenesis: a dynamic view.Stem cell therapies benefit Alport syndrome.A mouse Col4a4 mutation causing Alport glomerulosclerosis with abnormal collagen α3α4α5(IV) trimers.Deletion of von Hippel-Lindau in glomerular podocytes results in glomerular basement membrane thickening, ectopic subepithelial deposition of collagen {alpha}1{alpha}2{alpha}1(IV), expression of neuroglobin, and proteinuria.X-inactivation modifies disease severity in female carriers of murine X-linked Alport syndromeTransgenic expression of human LAMA5 suppresses murine Lama5 mRNA and laminin α5 protein deposition.Alport syndrome: abnormalities of type IV collagen genes and proteins.Collagen XIII induced in vascular endothelium mediates alpha1beta1 integrin-dependent transmigration of monocytes in renal fibrosisRenal fibrosis.Searching for a treatment for Alport syndrome using mouse modelsUpregulated expression of integrin α1 in mesangial cells and integrin α3 and vimentin in podocytes of Col4a3-null (Alport) miceModels of chronic kidney diseaseVitamin a deficiency and alterations in the extracellular matrix.Bone-marrow-derived stem cells repair basement membrane collagen defects and reverse genetic kidney disease.Biophysical properties of normal and diseased renal glomeruli.Transcriptional induction of slit diaphragm genes by Lmx1b is required in podocyte differentiation.New functional roles for non-collagenous domains of basement membrane collagensReduction of tumstatin in asthmatic airways contributes to angiogenesis, inflammation, and hyperresponsiveness.Matrix metalloproteinase dysregulation in the stria vascularis of mice with Alport syndrome: implications for capillary basement membrane pathology.Sequential expression of type IV collagen networks: testis as a model and relevance to spermatogenesisWnt/β-catenin pathway in podocytes integrates cell adhesion, differentiation, and survival.Investigating mechanisms of chronic kidney disease in mouse modelsAlphav beta6 integrin regulates renal fibrosis and inflammation in Alport mouse.Update of extracellular matrix, its receptors, and cell adhesion molecules in mammalian nephrogenesis.Minor Type IV Collagen α5 Chain Promotes Cancer Progression through Discoidin Domain Receptor-1.Type IV procollagen missense mutations associated with defects of the eye, vascular stability, the brain, kidney function and embryonic or postnatal viability in the mouse, Mus musculus: an extension of the Col4a1 allelic series and the identificatiGenetic elimination of α3(IV) collagen fails to rescue anti-collagen B cells.Mannose receptor 2 attenuates renal fibrosisGlomerular expression of type IV collagen chains in normal and X-linked Alport syndrome kidneys
P2860
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P2860
Molecular and functional defects in kidneys of mice lacking collagen alpha 3(IV): implications for Alport syndrome.
description
1996 nî lūn-bûn
@nan
1996年の論文
@ja
1996年論文
@yue
1996年論文
@zh-hant
1996年論文
@zh-hk
1996年論文
@zh-mo
1996年論文
@zh-tw
1996年论文
@wuu
1996年论文
@zh
1996年论文
@zh-cn
name
Molecular and functional defec ...... lications for Alport syndrome.
@ast
Molecular and functional defec ...... lications for Alport syndrome.
@en
type
label
Molecular and functional defec ...... lications for Alport syndrome.
@ast
Molecular and functional defec ...... lications for Alport syndrome.
@en
prefLabel
Molecular and functional defec ...... lications for Alport syndrome.
@ast
Molecular and functional defec ...... lications for Alport syndrome.
@en
P2860
P356
P1476
Molecular and functional defec ...... lications for Alport syndrome.
@en
P2093
P2860
P304
P356
10.1083/JCB.135.5.1403
P407
P577
1996-12-01T00:00:00Z