Pentamidine rescues contractility and rhythmicity in a Drosophila model of myotonic dystrophy heart dysfunction.
about
Drosophila tools and assays for the study of human diseasesExpanded CCUG repeat RNA expression in Drosophila heart and muscle trigger Myotonic Dystrophy type 1-like phenotypes and activate autophagocytosis genes.(CCUG)n RNA toxicity in a Drosophila model of myotonic dystrophy type 2 (DM2) activates apoptosis.Can Human Pluripotent Stem Cell-Derived Cardiomyocytes Advance Understanding of Muscular Dystrophies?Fruit flies on the front line: the translational impact of Drosophila.The Drosophila junctophilin gene is functionally equivalent to its four mammalian counterparts and is a modifier of a Huntingtin poly-Q expansion and the Notch pathway.Drosophila in the Heart of Understanding Cardiac Diseases: Modeling Channelopathies and Cardiomyopathies in the Fruitfly.Daunorubicin reduces MBNL1 sequestration caused by CUG-repeat expansion and rescues cardiac dysfunctions in a Drosophila model of myotonic dystrophy.Small Molecules Which Improve Pathogenesis of Myotonic Dystrophy Type 1.
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P2860
Pentamidine rescues contractility and rhythmicity in a Drosophila model of myotonic dystrophy heart dysfunction.
description
2015 nî lūn-bûn
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2015年の論文
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2015年論文
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2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
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2015年論文
@zh-tw
2015年论文
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2015年论文
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2015年论文
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name
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@ast
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@en
type
label
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@ast
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@en
prefLabel
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@ast
Pentamidine rescues contractil ...... c dystrophy heart dysfunction.
@en
P2093
P2860
P356
P1476
Pentamidine rescues contractil ...... ic dystrophy heart dysfunction
@en
P2093
Beatriz Llamusi
Estela Selma-Soriano
Juan Pablo Couso
Manuel Pérez-Alonso
Mouli Chakraborty
Ruben Artero
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P304
P356
10.1242/DMM.021428
P577
2015-10-29T00:00:00Z