Resistance to apoptosis caused by PIG-A gene mutations in paroxysmal nocturnal hemoglobinuria
about
Gpi19, the Saccharomyces cerevisiae homologue of mammalian PIG-P, is a subunit of the initial enzyme for glycosylphosphatidylinositol anchor biosynthesis.Leukemia arising out of paroxysmal nocturnal hemoglobinuria.Improved detection and characterization of paroxysmal nocturnal hemoglobinuria using fluorescent aerolysinIntectin, a novel small intestine-specific glycosylphosphatidylinositol-anchored protein, accelerates apoptosis of intestinal epithelial cells.PIG-A mutations in normal hematopoiesisA new aspect of the molecular pathogenesis of paroxysmal nocturnal hemoglobinuria.An X chromosome gene regulates hematopoietic stem cell kinetics.The small population of PIG-A mutant cells in myelodysplastic syndromes do not arise from multipotent hematopoietic stem cellsOCI-5/GPC3, a glypican encoded by a gene that is mutated in the Simpson-Golabi-Behmel overgrowth syndrome, induces apoptosis in a cell line-specific manner.Clonal populations of hematopoietic cells with paroxysmal nocturnal hemoglobinuria genotype and phenotype are present in normal individualsAdvances in the diagnosis and therapy of paroxysmal nocturnal hemoglobinuriaPotential link between MHC-self-peptide presentation and hematopoiesis; the analysis of HLA-DR expression in CD34-positive cells and self-peptide presentation repertoires of MHC molecules associated with paroxysmal nocturnal hemoglobinuria.Glycosylphosphatidylinositol-anchored protein deficiency confers resistance to apoptosis in PNH.Impaired growth and elevated fas receptor expression in PIGA(+) stem cells in primary paroxysmal nocturnal hemoglobinuriaSuccessful Treatment of Ascites using a Denver® Peritoneovenous Shunt in a Patient with Paroxysmal Nocturnal Hemoglobinuria and Budd-Chiari syndrome.The pathophysiology of paroxysmal nocturnal hemoglobinuria and treatment with eculizumab.Multidisciplinary clinical management of paroxysmal nocturnal hemoglobinuria.A GPI-anchored co-receptor for tissue factor pathway inhibitor controls its intracellular trafficking and cell surface expression.Enhanced cytotoxicity of rituximab following genetic and biochemical disruption of glycosylphosphatidylinositol anchored proteins.Antibody cross-linking of the glycosylphosphatidylinositol-linked protein CD59 on hematopoietic cells induces signaling pathways resembling activation by complement.Differential gene expression in hematopoietic progenitors from paroxysmal nocturnal hemoglobinuria patients reveals an apoptosis/immune response in 'normal' phenotype cells.Glycosylphosphatidylinositol (GPI) anchored protein deficiency serves as a reliable reporter of Pig-a gene Mutation: Support from an in vitro assay based on L5178Y/Tk+/- cells and the CD90.2 antigen.Glycosylphosphatidylinositol (GPI)-deficient Jurkat T cells as a model to study functions of GPI-anchored proteins.
P2860
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P2860
Resistance to apoptosis caused by PIG-A gene mutations in paroxysmal nocturnal hemoglobinuria
description
1997 nî lūn-bûn
@nan
1997年の論文
@ja
1997年論文
@yue
1997年論文
@zh-hant
1997年論文
@zh-hk
1997年論文
@zh-mo
1997年論文
@zh-tw
1997年论文
@wuu
1997年论文
@zh
1997年论文
@zh-cn
name
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@ast
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@en
type
label
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@ast
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@en
prefLabel
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@ast
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@en
P2093
P2860
P356
P1476
Resistance to apoptosis caused ...... ysmal nocturnal hemoglobinuria
@en
P2093
P2860
P304
P356
10.1073/PNAS.94.16.8756
P407
P577
1997-08-01T00:00:00Z