Acidic pH increases airway surface liquid viscosity in cystic fibrosis
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pH Dependent Antimicrobial Peptides and Proteins, Their Mechanisms of Action and Potential as Therapeutic AgentsCFTR Modulators: Shedding Light on Precision Medicine for Cystic FibrosisDiffusion through Pig Gastric Mucin: Effect of Relative HumidityMarked increases in mucociliary clearance produced by synergistic secretory agonists or inhibition of the epithelial sodium channel.Aspergillosis and the role of mucins in cystic fibrosisGel-forming mucins form distinct morphologic structures in airwaysCystic fibrosis lung environment and Pseudomonas aeruginosa infection.Electrolyte transport properties in distal small airways from cystic fibrosis pigs with implications for host defense.Relationships among CFTR expression, HCO3- secretion, and host defense may inform gene- and cell-based cystic fibrosis therapiesRepurposing tromethamine as inhaled therapy to treat CF airway disease.CFTR gene transfer with AAV improves early cystic fibrosis pig phenotypesRole of CFTR in epithelial physiology.Contribution of mucus concentration and secreted mucins Muc5ac and Muc5b to the pathogenesis of muco-obstructive lung diseaseDefective postsecretory maturation of MUC5B mucin in cystic fibrosis airwaysThe Mucus Barrier to Inhaled Gene Therapy.Gene delivery to the lungs: pulmonary gene therapy for cystic fibrosis.Acidosis increases the susceptibility of respiratory epithelial cells to Pseudomonas aeruginosa-induced cytotoxicity.Particle-Tracking Microrheology Using Micro-Optical Coherence Tomography.Strategies for the etiological therapy of cystic fibrosis.Use of ferrets for electrophysiologic monitoring of ion transport.Airway surface liquid pH is not acidic in children with cystic fibrosis.An integrated mathematical epithelial cell model for airway surface liquid regulation by mechanical forces.Solitary Cholinergic Stimulation Induces Airway Hyperreactivity and Transcription of Distinct Pro-inflammatory Pathways.Nominal carbonic anhydrase activity minimizes airway-surface liquid pH changes during breathing.Motile cilia of human airway epithelia contain hedgehog signaling components that mediate noncanonical hedgehog signaling.Imaging viscosity of intragranular mucin matrix in cystic fibrosis cells.Development of an airway mucus defect in the cystic fibrosis rat.Physicochemical properties of mucus and their impact on transmucosal drug delivery.Qualitative metabolomics profiling of serum and bile from dogs with gallbladder mucocele formation.Airway Mucus and Asthma: The Role of MUC5AC and MUC5B.Impaired PGE2-stimulated Cl- and HCO3- secretion contributes to cystic fibrosis airway disease.ATP12A promotes mucus dysfunction during Type 2 airway inflammation.SPX-101 Is a Promising and Novel Nebulized ENaC Inhibitor.Thymosin α1: a single drug with multiple targets in cystic fibrosis.Airway Epithelium Dysfunction in Cystic Fibrosis and COPD.The EGFR-ADAM17 Axis in Chronic Obstructive Pulmonary Disease and Cystic Fibrosis Lung Pathology.Airway Epithelial Cell Function and Respiratory Host Defense in Chronic Obstructive Pulmonary Disease.Molecular basis of cystic fibrosis: from bench to bedsideMucins: the frontline defence of the lungWidespread airway distribution and short-term phenotypic correction of cystic fibrosis pigs following aerosol delivery of piggyBac/adenovirus
P2860
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P2860
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
description
2016 nî lūn-bûn
@nan
2016年の論文
@ja
2016年論文
@yue
2016年論文
@zh-hant
2016年論文
@zh-hk
2016年論文
@zh-mo
2016年論文
@zh-tw
2016年论文
@wuu
2016年论文
@zh
2016年论文
@zh-cn
name
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@ast
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@en
type
label
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@ast
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@en
prefLabel
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@ast
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@en
P2093
P2860
P356
P1476
Acidic pH increases airway surface liquid viscosity in cystic fibrosis
@en
P2093
Ajit Varki
Biswa Choudhury
James D McMenimen
Mark J Hoegger
Michael J Welsh
Philip H Karp
Thomas O Moninger
Xiao Xiao Tang
P2860
P304
P356
10.1172/JCI83922
P407
P577
2016-01-25T00:00:00Z