Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
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Functional changes in pulmonary arterial endothelial cells associated with BMPR2 mutationsTargeting BMP signalling in cardiovascular disease and anaemiaThe molecular genetics and cellular mechanisms underlying pulmonary arterial hypertensionMicrovascular repair: post-angiogenesis vascular dynamicsThe genetics of pulmonary arterial hypertensionA brief overview of mouse models of pulmonary arterial hypertension: problems and prospects.Endoglin-mediated suppression of prostate cancer invasion is regulated by activin and bone morphogenetic protein type II receptors.Gene expression in lungs of mice lacking the 5-hydroxytryptamine transporter gene.Adenosine A2B receptor and hyaluronan modulate pulmonary hypertension associated with chronic obstructive pulmonary diseaseDevelopment of pulmonary arterial hypertension in women: interplay of sex hormones and pulmonary vascular disease.Interaction between bone morphogenetic protein receptor type 2 and estrogenic compounds in pulmonary arterial hypertensionSubcellular mechanisms in pulmonary arterial hypertension: combinatorial modalities that inhibit anterograde trafficking and cause bone morphogenetic protein receptor type 2 mislocalization.Altered gene expression in pulmonary tissue of tryptophan hydroxylase-1 knockout mice: implications for pulmonary arterial hypertension.Role of BMPR2 alternative splicing in heritable pulmonary arterial hypertension penetrance.BMPR2 mutation alters the lung macrophage endothelin-1 cascade in a mouse model and patients with heritable pulmonary artery hypertension.Bone Morphogenetic Protein (BMP) signaling in development and human diseasesModification of hemodynamic and immune responses to exposure with a weak antigen by the expression of a hypomorphic BMPR2 genePulmonary hypertension in women.Deletion of the sequence encoding the tail domain of the bone morphogenetic protein type 2 receptor reveals a bone morphogenetic protein 7-specific gain of functionPhysiologic and molecular consequences of endothelial Bmpr2 mutation.Paigen diet-fed apolipoprotein E knockout mice develop severe pulmonary hypertension in an interleukin-1-dependent manner.Rescuing the BMPR2 signaling axis in pulmonary arterial hypertensionThe genetics of pulmonary arterial hypertension in the post-BMPR2 era.Idiopathic and heritable PAH perturb common molecular pathways, correlated with increased MSX1 expression.Cytoskeletal defects in Bmpr2-associated pulmonary arterial hypertensionSerotonin 2B Receptor Antagonism Prevents Heritable Pulmonary Arterial Hypertension.Metabolomic analysis of bone morphogenetic protein receptor type 2 mutations in human pulmonary endothelium reveals widespread metabolic reprogramming.Expression of mutant bone morphogenetic protein receptor II worsens pulmonary hypertension secondary to pulmonary fibrosis.Estrogen Metabolite 16α-Hydroxyestrone Exacerbates Bone Morphogenetic Protein Receptor Type II-Associated Pulmonary Arterial Hypertension Through MicroRNA-29-Mediated Modulation of Cellular MetabolismRaf/ERK drives the proliferative and invasive phenotype of BMPR2-silenced pulmonary artery endothelial cells.Right ventricular systolic pressure measurements in combination with harvest of lung and immune tissue samples in mice.Pulmonary Arterial Hypertension: A Current Perspective on Established and Emerging Molecular Genetic Defects.Endothelial HIF signaling regulates pulmonary fibrosis-associated pulmonary hypertension.The A2B adenosine receptor modulates pulmonary hypertension associated with interstitial lung disease.Bone Marrow-derived Cells Contribute to the Pathogenesis of Pulmonary Arterial Hypertension.The Endothelial Prolyl-4-Hydroxylase Domain 2/Hypoxia-Inducible Factor 2 Axis Regulates Pulmonary Artery Pressure in Mice.SMAD1 deficiency in either endothelial or smooth muscle cells can predispose mice to pulmonary hypertensionA potential role for insulin resistance in experimental pulmonary hypertensionRho-kinase inhibition alleviates pulmonary hypertension in transgenic mice expressing a dominant-negative type II bone morphogenetic protein receptor gene.Defective pulmonary vascular remodeling in Smad8 mutant mice
P2860
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P2860
Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
description
2008 nî lūn-bûn
@nan
2008年の論文
@ja
2008年論文
@yue
2008年論文
@zh-hant
2008年論文
@zh-hk
2008年論文
@zh-mo
2008年論文
@zh-tw
2008年论文
@wuu
2008年论文
@zh
2008年论文
@zh-cn
name
Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
@en
type
label
Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
@en
prefLabel
Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
@en
P2093
P2860
P1476
Mice expressing BMPR2R899X transgene in smooth muscle develop pulmonary vascular lesions.
@en
P2093
Brian Ickes
Daniel Crona
Duncan Stewart
James West
Julie Harral
Karen Fagan
Sebastian Albu
P2860
P304
P356
10.1152/AJPLUNG.90255.2008
P577
2008-08-22T00:00:00Z