The immotile-cilia syndrome. A congenital ciliary abnormality as an etiologic factor in chronic airway infections and male sterility.
about
An X-linked gene encodes a major human sperm fibrous sheath protein, hAKAP82. Genomic organization, protein kinase A-RII binding, and distribution of the precursor in the sperm tailRole of macrophage-stimulating protein and its receptor, RON tyrosine kinase, in ciliary motilityYoung's syndrome. An association between male sterility and bronchiectasis.Incidence of Legionella pneumophila infections among Oklahoma pulmonary disease patientsGenetics and biology of primary ciliary dyskinesiaIsolation and genetic characterization of mother-of-snow-white, a maternal effect allele affecting laterality and lateralized behaviors in zebrafishPrimary ciliary dyskinesia.The axoneme: the propulsive engine of spermatozoa and cilia and associated ciliopathies leading to infertilityYoung's syndrome associated with situs inversus totalisIsolation and properties of Gas8, a growth arrest-specific gene regulated during male gametogenesis to produce a protein associated with the sperm motility apparatusDelayed irradiation effects on nasal epithelium in patients with nasopharyngeal carcinoma. An ultrastructural study.The oocyte activation and Ca2+ oscillation-inducing abilities of mouse and human dead (sonicated) spermatozoa.Cep70 and Cep131 contribute to ciliogenesis in zebrafish embryos.Recurrent chest infections, ciliary abnormalities and partial complement deficiency in a Jordanian familyLegionella brain stem encephalopathy and peripheral neuropathy without preceding pneumoniaAbsence of central functional cholinergic deficits in myasthenia gravis.Primary Ciliary Dyskinesia: An Update on Clinical Aspects, Genetics, Diagnosis, and Future Treatment StrategiesVariations in the ultrastructure of human nasal cilia including abnormalities found in retinitis pigmentosa.Germline mutations in an intermediate chain dynein cause primary ciliary dyskinesia.An explanation for the seasonality of acute upper respiratory tract viral infections.Classification of left-right patterning defects in zebrafish, mice, and humans.Lung mucus production and mucociliary clearance: methods of assessment.Structural heterogeneity of the axonemes of respiratory cilia and sperm flagella in normal men.Mucociliary transport using 99mTc-albumin colloid: a reliable screening test for primary ciliary dyskinesia.Transmission electron microscopy in the diagnosis of primary ciliary dyskinesia.Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosisClinical and genetic aspects of primary ciliary dyskinesia/Kartagener syndrome.Reduction of ciliary beat frequency in vitro by sputum from patients with bronchiectasis: a serine proteinase effect.Mechanical control of tissue morphogenesis.Ultrastructural abnormalities of bronchial cilia in children with recurrent airway infections and bronchiectasis.Semen analysis.Unique among ciliopathies: primary ciliary dyskinesia, a motile cilia disorder.Measurement of nasal mucociliary clearancePrimary Ciliary Dyskinesia in Children: A Review for Pediatricians, Allergists, and Pediatric Pulmonologists.Ultrastructure of respiratory cilia of WIC-Hyd male rats. An animal model for human immotile cilia syndromeThe role of cytoskeletal and cytocontractile elements in pathologic processes.Ciliary dyskinesia with normal ultrastructure.Respiratory tract disease and obstructive azoospermiaBronchiectasis and oligospermia: two families.Legionnaires' disease: a review of 79 community acquired cases in Nottingham.
P2860
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P2860
The immotile-cilia syndrome. A congenital ciliary abnormality as an etiologic factor in chronic airway infections and male sterility.
description
1977 nî lūn-bûn
@nan
1977年の論文
@ja
1977年論文
@yue
1977年論文
@zh-hant
1977年論文
@zh-hk
1977年論文
@zh-mo
1977年論文
@zh-tw
1977年论文
@wuu
1977年论文
@zh
1977年论文
@zh-cn
name
The immotile-cilia syndrome. A ...... infections and male sterility.
@en
type
label
The immotile-cilia syndrome. A ...... infections and male sterility.
@en
prefLabel
The immotile-cilia syndrome. A ...... infections and male sterility.
@en
P2093
P1476
The immotile-cilia syndrome. A ...... infections and male sterility.
@en
P2093
Afzelius BA
Eliasson R
Mossberg B
P356
10.1056/NEJM197707072970101
P407
P577
1977-07-01T00:00:00Z