Secretion of phosphomannosyl-deficient arylsulphatase A and cathepsin D from isolated human macrophages
about
Defective endoplasmic reticulum-resident membrane protein CLN6 affects lysosomal degradation of endocytosed arylsulfatase AIncreased expression of lysosomal acid phosphatase in CLN3-defective cells and mouse brain tissueMucolipidosis II is caused by mutations in GNPTA encoding the alpha/beta GlcNAc-1-phosphotransferaseCorrection of metachromatic leukodystrophy in the mouse model by transplantation of genetically modified hematopoietic stem cells.Gene therapy of metachromatic leukodystrophy reverses neurological damage and deficits in mice.Gene therapy of metachromatic leukodystrophy.Glycosylation- and phosphorylation-dependent intracellular transport of lysosomal hydrolases.Proteolytic processing of the gamma-subunit is associated with the failure to form GlcNAc-1-phosphotransferase complexes and mannose 6-phosphate residues on lysosomal enzymes in human macrophages.Lrp1/LDL Receptor Play Critical Roles in Mannose 6-Phosphate-Independent Lysosomal Enzyme Targeting.
P2860
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P2860
Secretion of phosphomannosyl-deficient arylsulphatase A and cathepsin D from isolated human macrophages
description
2002 nî lūn-bûn
@nan
2002年の論文
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2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
2002年论文
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2002年论文
@zh-cn
name
Secretion of phosphomannosyl-d ...... rom isolated human macrophages
@en
type
label
Secretion of phosphomannosyl-d ...... rom isolated human macrophages
@en
prefLabel
Secretion of phosphomannosyl-d ...... rom isolated human macrophages
@en
P2093
P2860
P356
P1433
P1476
Secretion of phosphomannosyl-d ...... rom isolated human macrophages
@en
P2093
Kurt Ullrich
Nicole Muschol
Stephan Tiede
Thomas Braulke
Ulrich Matzner
Volkmar Gieselmann
P2860
P304
P356
10.1042/BJ20020249
P407
P577
2002-12-01T00:00:00Z