Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
about
Structural effects of fibulin 5 missense mutations associated with age-related macular degeneration and cutis laxaLatent TGF-β binding protein-2 is essential for the development of ciliary zonule microfibrilsDifferential regulation of elastic fiber formation by fibulin-4 and -5Latent TGF-beta-binding protein 2 binds to DANCE/fibulin-5 and regulates elastic fiber assemblyFibulin 5 forms a compact dimer in physiological solutions.A novel intracellular fibulin-1D variant binds to the cytoplasmic domain of integrin beta 1 subunitGenetic heterogeneity of cutis laxa: a heterozygous tandem duplication within the fibulin-5 (FBLN5) gene.Fibulin-4: a novel gene for an autosomal recessive cutis laxa syndromeFibulin-4 regulates expression of the tropoelastin gene and consequent elastic-fibre formation by human fibroblastsCell adhesion to tropoelastin is mediated via the C-terminal GRKRK motif and integrin alphaVbeta3The Extracellular Matrix in Bronchopulmonary Dysplasia: Target and SourceMatrix control of transforming growth factor-β functionCharacterization of Microfibrillar-associated Protein 4 (MFAP4) as a Tropoelastin- and Fibrillin-binding Protein Involved in Elastic Fiber FormationFibulin-5 interacts with fibrillin-1 molecules and microfibrilsFibulin-5 gene expression in human lung fibroblasts is regulated by TGF-beta and phosphatidylinositol 3-kinase activityLactadherin binds to elastin--a starting point for medin amyloid formation?Microfibril-associated MAGP-2 stimulates elastic fiber assemblyNeutrophil elastase-initiated EGFR/MEK/ERK signaling counteracts stabilizing effect of autocrine TGF-beta on tropoelastin mRNA in lung fibroblastsMouse homologue of skin-specific retroviral-like aspartic protease involved in wrinkle formationEMILIN-1 deficiency induces elastogenesis and vascular cell defectsCutis laxa: intersection of elastic fiber biogenesis, TGFβ signaling, the secretory pathway and metabolismLarge-scale candidate gene analysis of HDL particle featuresModeling autosomal recessive cutis laxa type 1C in mice reveals distinct functions for Ltbp-4 isoformsThe extracellular matrix in development and morphogenesis: a dynamic view.Knockout mice: is it just genetics? Effect of enriched housing on fibulin-4(+/-) mice.Fibulin-2 and fibulin-5 cooperatively function to form the internal elastic lamina and protect from vascular injury.Consistent biomechanical phenotyping of common carotid arteries from seven genetic, pharmacological, and surgical mouse models.Quantification of pelvic organ prolapse in mice: vaginal protease activity precedes increased MOPQ scores in fibulin 5 knockout miceDefining elastic fiber interactions by molecular fishing: an affinity purification and mass spectrometry approach.Fibulin-4 is essential for maintaining arterial wall integrity in conduit but not muscular arteries.Biogenesis and function of fibrillin assemblies.Plasma levels of S100A4 in portopulmonary hypertensionExtracellular matrix molecules facilitating vascular biointegrationFibulin-4 deficiency results in ascending aortic aneurysms: a potential link between abnormal smooth muscle cell phenotype and aneurysm progressionExtracellular matrix molecules: potential targets in pharmacotherapy.Expression, purification, and characterization of recombinant fibulin-5 in a prokaryote expression system.Quantitative proteomics analysis of chondrogenic differentiation of C3H10T1/2 mesenchymal stem cells by iTRAQ labeling coupled with on-line two-dimensional LC/MS/MS.Altered vascular remodeling in fibulin-5-deficient mice reveals a role of fibulin-5 in smooth muscle cell proliferation and migration.Clinical presentation of a patient with localized acquired cutis laxa of abdomen: a case reportUnraveling the mechanism of elastic fiber assembly: The roles of short fibulins
P2860
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P2860
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
description
2002 nî lūn-bûn
@nan
2002 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2002 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2002年の論文
@ja
2002年論文
@yue
2002年論文
@zh-hant
2002年論文
@zh-hk
2002年論文
@zh-mo
2002年論文
@zh-tw
2002年论文
@wuu
name
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@ast
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en-gb
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@nl
type
label
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@ast
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en-gb
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@nl
prefLabel
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@ast
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en-gb
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@nl
P2093
P3181
P356
P1433
P1476
Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo
@en
P2093
Barry C Starcher
Elaine C Davis
Eric N Olson
Hiromi Yanagisawa
James A Richardson
Masashi Yanagisawa
Takashi Ouchi
P2888
P304
P3181
P356
10.1038/415168A
P407
P577
2002-01-10T00:00:00Z
P6179
1030584328