The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Delta mutant. Implications for Barth syndrome
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Cardiolipin signaling mechanisms: collapse of asymmetry and oxidationComparison of lymphoblast mitochondria from normal subjects and patients with Barth syndrome using electron microscopic tomographyDisruption of the phosphatidylserine decarboxylase gene in mice causes embryonic lethality and mitochondrial defectsCharacterization of tafazzin splice variants from humans and fruit fliesLoss of NAD(H) from swollen yeast mitochondria.Barth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell StudiesMitochondrial mislocalization and altered assembly of a cluster of Barth syndrome mutant tafazzinsCardiolipin mediates cross-talk between mitochondria and the vacuole.Identification of a cardiolipin-specific phospholipase encoded by the gene CLD1 (YGR110W) in yeastTaz1, an outer mitochondrial membrane protein, affects stability and assembly of inner membrane protein complexes: implications for Barth SyndromeAim24 and MICOS modulate respiratory function, tafazzin-related cardiolipin modification and mitochondrial architectureThe enzymatic function of tafazzinCellular functions of cardiolipin in yeastCardiolipin remodeling: a regulatory hub for modulating cardiolipin metabolism and functionBacteria, yeast, worms, and flies: exploiting simple model organisms to investigate human mitochondrial diseasesKnown unknowns of cardiolipin signaling: the best is yet to comeElimination of the unnecessary: intra- and extracellular signaling by anionic phospholipidsCardiolipin, a critical determinant of mitochondrial carrier protein assembly and function.Distinct effects of tafazzin deletion in differentiated and undifferentiated mitochondria.Loss of function of KRE5 suppresses temperature sensitivity of mutants lacking mitochondrial anionic lipidsMitochondria-targeted antioxidant prevents cardiac dysfunction induced by tafazzin gene knockdown in cardiac myocytes.Lipidomics of intact mitochondria by MALDI-TOF/MSLoss of cardiac tetralinoleoyl cardiolipin in human and experimental heart failure.A Drosophila model of Barth syndromeBarth syndrome mutations that cause tafazzin complex lability.Cardiolipin affects the supramolecular organization of ATP synthase in mitochondria.Specific degradation of phosphatidylglycerol is necessary for proper mitochondrial morphology and functionLoss of cardiolipin leads to perturbation of mitochondrial and cellular iron homeostasisRole of cardiolipin alterations in mitochondrial dysfunction and disease.Barth syndrome, a human disorder of cardiolipin metabolism.Seven functional classes of Barth syndrome mutationCardiolipin synthesis for the assembly of bacterial and mitochondrial membranes.Cardiolipin defines the interactome of the major ADP/ATP carrier protein of the mitochondrial inner membraneThe physical state of lipid substrates provides transacylation specificity for tafazzinCardiolipin biosynthesis and remodeling enzymes are altered during development of heart failure.The power of yeast to model diseases of the powerhouse of the cell.Unremodeled and remodeled cardiolipin are functionally indistinguishable in yeast.Cardiolipin-dependent formation of mitochondrial respiratory supercomplexes.Persistent pulmonary hypertension results in reduced tetralinoleoyl-cardiolipin and mitochondrial complex II + III during the development of right ventricular hypertrophy in the neonatal pig heart.Characterization of lymphoblast mitochondria from patients with Barth syndrome.
P2860
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P2860
The human TAZ gene complements mitochondrial dysfunction in the yeast taz1Delta mutant. Implications for Barth syndrome
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2004 nî lūn-bûn
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2004 թուականի Հոկտեմբերին հրատարակուած գիտական յօդուած
@hyw
2004 թվականի հոտեմբերին հրատարակված գիտական հոդված
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2004年の論文
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2004年論文
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2004年論文
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2004年論文
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2004年論文
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2004年論文
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2004年论文
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name
The human TAZ gene complements ...... mplications for Barth syndrome
@ast
The human TAZ gene complements ...... mplications for Barth syndrome
@en
The human TAZ gene complements ...... mplications for Barth syndrome
@en-gb
The human TAZ gene complements ...... mplications for Barth syndrome
@nl
type
label
The human TAZ gene complements ...... mplications for Barth syndrome
@ast
The human TAZ gene complements ...... mplications for Barth syndrome
@en
The human TAZ gene complements ...... mplications for Barth syndrome
@en-gb
The human TAZ gene complements ...... mplications for Barth syndrome
@nl
prefLabel
The human TAZ gene complements ...... mplications for Barth syndrome
@ast
The human TAZ gene complements ...... mplications for Barth syndrome
@en
The human TAZ gene complements ...... mplications for Barth syndrome
@en-gb
The human TAZ gene complements ...... mplications for Barth syndrome
@nl
P2093
P921
P356
P1476
The human TAZ gene complements ...... mplications for Barth syndrome
@en
P2093
Frederic M Vaz
Miriam L Greenberg
Zhiming Gu
P304
P356
10.1074/JBC.M405479200
P407
P577
2004-10-22T00:00:00Z