Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid β-oxidation
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How to move an amphipathic molecule across a lipid bilayer: different mechanisms for different ABC transporters?Peroxisomal ABC transporters: functions and mechanismABC Transporter Subfamily D: Distinct Differences in Behavior between ABCD1-3 and ABCD4 in Subcellular Localization, Function, and Human DiseaseThe Concise Guide to PHARMACOLOGY 2013/14: transporters.Barley has two peroxisomal ABC transporters with multiple functions in β-oxidationStructure-function analysis of peroxisomal ATP-binding cassette transporters using chimeric dimers.Abcd2 is a strong modifier of the metabolic impairments in peritoneal macrophages of ABCD1-deficient miceABCD2 alters peroxisome proliferator-activated receptor α signaling in vitro, but does not impair responses to fenofibrate therapy in a mouse model of diet-induced obesityPathophysiology of X-linked adrenoleukodystrophy.Histone deacetylase inhibitor upregulates peroxisomal fatty acid oxidation and inhibits apoptotic cell death in abcd1-deficient glial cells.Mammalian peroxisomal ABC transporters: from endogenous substrates to pathology and clinical significance.The absence of ABCD2 sensitizes mice to disruptions in lipid metabolism by dietary erucic acid.Intrinsic acyl-CoA thioesterase activity of a peroxisomal ATP binding cassette transporter is required for transport and metabolism of fatty acidsImpaired very long-chain acyl-CoA β-oxidation in human X-linked adrenoleukodystrophy fibroblasts is a direct consequence of ABCD1 transporter dysfunction.A Novel Double Mutation in the ABCD1 Gene in a Patient with X-linked Adrenoleukodystrophy: Analysis of the Stability and Function of the Mutant ABCD1 Protein.The peroxisome: an update on mysteries.Advances and pitfalls of cell therapy in metabolic leukodystrophies.Peroxisome-mitochondria interplay and disease.Functional characterisation of peroxisomal β-oxidation disorders in fibroblasts using lipidomics.Predictive Structure and Topology of Peroxisomal ATP-Binding Cassette (ABC) Transporters.Peroxisomal ATP-binding cassette transporters form mainly tetramers.Substrate specificity overlap and interaction between adrenoleukodystrophy protein (ALDP/ABCD1) and adrenoleukodystrophy-related protein (ALDRP/ABCD2).Carnitine transport and fatty acid oxidation.Translocation of the ABC transporter ABCD4 from the endoplasmic reticulum to lysosomes requires the escort protein LMBD1.Peroxisomal fatty acid uptake mechanism in Saccharomyces cerevisiae.High-grade ovarian serous carcinoma patients exhibit profound alterations in lipid metabolism.Erucic acid in feed and foodEffect of Lorenzo's Oil on Hepatic Gene Expression and the Serum Fatty Acid Level in abcd1-Deficient Mice.ABC transportome inventory of human pathogenic yeast Candida glabrata: Phylogenetic and expression analysis
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P248
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P2860
Differential substrate specificities of human ABCD1 and ABCD2 in peroxisomal fatty acid β-oxidation
description
2011 nî lūn-bûn
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2011 թուականի Մարտին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի մարտին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@ast
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en-gb
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@nl
type
label
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@ast
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en-gb
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@nl
prefLabel
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@ast
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en-gb
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@nl
P2093
P921
P3181
P1476
Differential substrate specifi ...... xisomal fatty acid β-oxidation
@en
P2093
Carlo W T van Roermund
Hans R Waterham
Lodewijk Ijlst
Wouter F Visser
P304
P3181
P356
10.1016/J.BBALIP.2010.11.010
P407
P577
2011-03-01T00:00:00Z