Distinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiency
about
Skeletal muscle laminin and MDC1A: pathogenesis and treatment strategies.Basement membranes: cell scaffoldings and signaling platforms.Transgenic expression of Laminin α1 chain does not prevent muscle disease in the mdx mouse model for Duchenne muscular dystrophy.Muscle-specific expression of insulin-like growth factor 1 improves outcome in Lama2Dy-w mice, a model for congenital muscular dystrophy type 1AQuantitative proteomic analysis reveals metabolic alterations, calcium dysregulation, and increased expression of extracellular matrix proteins in laminin α2 chain-deficient muscle.Chronic nerve compression alters Schwann cell myelin architecture in a murine model.Laminin-111 protein therapy reduces muscle pathology and improves viability of a mouse model of merosin-deficient congenital muscular dystrophySchwann cell myelination requires integration of laminin activities.Laminin-211 in skeletal muscle function.Integrins in renal development.Glia unglued: how signals from the extracellular matrix regulate the development of myelinating glia.The dystrophin-glycoprotein complex in the prevention of muscle damage.Human pathogens utilize host extracellular matrix proteins laminin and collagen for adhesion and invasion of the host.The myotomal basement membrane: insight into laminin-111 function and its control by Sonic hedgehog signaling.Non-redundant function of dystroglycan and β1 integrins in radial sorting of axons.Laminin: loss-of-function studies.Deletion of integrin α7 subunit does not aggravate the phenotype of laminin α2 chain-deficient mice.Laminin-111 improves muscle repair in a mouse model of merosin-deficient congenital muscular dystrophy.Laminin differentially regulates the stemness of type I and type II pericytes.Integrin signaling, cell survival, and anoikis: distinctions, differences, and differentiation.Proteasome inhibition improves the muscle of laminin α2 chain-deficient mice.Autophagy is increased in laminin α2 chain-deficient muscle and its inhibition improves muscle morphology in a mouse model of MDC1A.
P2860
Q22001192-D3DB13F7-9238-4559-B90C-8F1933DCC430Q34576367-0418C6C1-466A-4E70-81EE-0DD1251AEF01Q34805388-2110C7A4-2FB8-4FC4-8630-DB6B90B82908Q34994784-CB4D0630-3934-4305-BF13-AB7D4E9F13D5Q35201194-7011C4F9-C4DA-41DD-B897-B9C669FC51C4Q35685137-622200BE-9641-4BEA-B588-1A08A75ACE0EQ35952091-2A7F3F37-D254-4E67-B8A9-14A2117210B6Q36407316-982C6FB0-9590-4B29-B2E3-C77B9F3CCA20Q36531788-B74A52C4-840A-45FA-94AB-DC72B1E6D405Q37878382-EA7AC7F3-AE31-4E76-AD53-6DF60776EBAFQ37915435-7C389648-3C8D-4D88-9189-0B378741A52DQ37946876-867010E4-CAED-4B8F-AA67-0E6EEE72289CQ38005762-7EBD4AEA-E1F8-4EFA-9AD5-FA64E2598B42Q38071469-8BB24DBC-C97D-41FD-A1B8-505C6280D1B6Q38254331-24BB70D1-DA8E-4DC9-B1BB-41EBD4189AECQ38815433-C7CF774C-18D0-405E-B130-8AA51ADE5A7BQ40556372-FE7EB489-20A6-4BF8-899A-061DB4BAA020Q41881081-5A90F988-5F97-4A73-990B-2F21684D1488Q42323278-A0DB4ADA-4C46-45CD-9310-8D4DE23A3A2EQ42826052-79E8C889-02DE-4770-9845-29AE15B42832Q54401460-86FB13D6-C083-4F7C-B11B-D6E14E43D724Q54560138-3C0FEB34-C210-4971-B9A4-1DC43A5A121D
P2860
Distinct roles for laminin globular domains in laminin alpha1 chain mediated rescue of murine laminin alpha2 chain deficiency
description
2010 nî lūn-bûn
@nan
2010 թուականին հրատարակուած գիտական յօդուած
@hyw
2010 թվականին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@ast
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@en
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@nl
type
label
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@ast
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@en
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@nl
prefLabel
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@ast
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@en
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@nl
P2093
P2860
P1433
P1476
Distinct roles for laminin glo ...... aminin alpha2 chain deficiency
@en
P2093
Harri Elamaa
Kinga I Gawlik
Madeleine Durbeej
Mikael Akerlund
Virginie Carmignac
P2860
P304
P356
10.1371/JOURNAL.PONE.0011549
P407
P577
2010-01-01T00:00:00Z