The proteolipid protein gene and myelin disorders in man and animal models
about
Function of quaking in myelination: regulation of alternative splicing.The role of neuronal complexes in human X-linked brain diseasesOligodendrocytes expressing exclusively the DM20 isoform of the proteolipid protein gene: myelination and developmentInduction of axon growth arrest without growth cone collapse through the N-terminal region of four-transmembrane glycoprotein M6aDiffusion tensor imaging of patients with proteolipid protein 1 gene mutations.New mutation of pelizaeus--merzbacher-like disease; a report from iran.Disease-associated mutations cause premature oligomerization of myelin proteolipid protein in the endoplasmic reticulum.Axon-glial interaction in the CNS: what we have learned from mouse models of Pelizaeus-Merzbacher disease.Membrane traffic in myelinating oligodendrocytes.CNS myelination and PLP gene dosage.Insertion of mutant proteolipid protein results in missorting of myelin proteins.Functional genomic and proteomic analysis reveals disruption of myelin-related genes and translation in a mouse model of early life neglectScience in motion: common molecular pathological themes emerge in the hereditary spastic paraplegiasRole of Proteolipid Protein in HSV-1 Entry in Oligodendrocytic Cells.Expression of a myelin proteolipid protein (Plp)-lacZ transgene is reduced in both the CNS and PNS of Plp(jp) mice.Survival of, and competition between, oligodendrocytes expressing different alleles of the Plp gene.Mutation in the myelin proteolipid protein gene alters BK and SK channel function in the caudal medulla.The molecular and cellular defects underlying Pelizaeus-Merzbacher disease.Protecting axons in multiple sclerosis.Differences in endoplasmic-reticulum quality control determine the cellular response to disease-associated mutants of proteolipid protein.Cellular Pathology of Pelizaeus-Merzbacher Disease Involving Chaperones Associated with Endoplasmic Reticulum StressProgesterone antagonist therapy in a Pelizaeus-Merzbacher mouse model.Mitochondrial protein translocases for survival and wellbeing.Peripheral myelin protein 22 alters membrane architecture.Rumpshaker-like proteolipid protein (PLP) ratio in a mouse model with unperturbed structural and functional integrity of the myelin sheath and axons in the central nervous system.Patients lacking the major CNS myelin protein, proteolipid protein 1, develop length-dependent axonal degeneration in the absence of demyelination and inflammation.Severe Convulsions and Dysmyelination in Both Jimpy and Cx32/47 -/- Mice may Associate Astrocytic L-Channel Function with Myelination and Oligodendrocytic Connexins with Internodal Kv Channels.Chemical Screening Identifies Enhancers of Mutant Oligodendrocyte Survival and Unmasks a Distinct Pathological Phase in Pelizaeus-Merzbacher Disease
P2860
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P2860
The proteolipid protein gene and myelin disorders in man and animal models
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2000 nî lūn-bûn
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2000 թուականի Ապրիլին հրատարակուած գիտական յօդուած
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2000 թվականի ապրիլին հրատարակված գիտական հոդված
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2000年の論文
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2000年論文
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2000年論文
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2000年論文
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2000年論文
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2000年論文
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2000年论文
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The proteolipid protein gene and myelin disorders in man and animal models
@ast
The proteolipid protein gene and myelin disorders in man and animal models
@en
The proteolipid protein gene and myelin disorders in man and animal models
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type
label
The proteolipid protein gene and myelin disorders in man and animal models
@ast
The proteolipid protein gene and myelin disorders in man and animal models
@en
The proteolipid protein gene and myelin disorders in man and animal models
@nl
prefLabel
The proteolipid protein gene and myelin disorders in man and animal models
@ast
The proteolipid protein gene and myelin disorders in man and animal models
@en
The proteolipid protein gene and myelin disorders in man and animal models
@nl
P2093
P356
P1476
The proteolipid protein gene and myelin disorders in man and animal models
@en
P2093
P304
P356
10.1093/HMG/9.6.987
P407
P50
P577
2000-04-01T00:00:00Z