The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin
about
Specific interaction of the actin-binding domain of dystrophin with intermediate filaments containing keratin 19.The actin gene family: function follows isoformDevelopmental and pathogenic mechanisms of basement membrane assemblySorting of a nonmuscle tropomyosin to a novel cytoskeletal compartment in skeletal muscle results in muscular dystrophyMechanosensitive channel properties and membrane mechanics in mouse dystrophic myotubesOverexpression of Latent TGFβ Binding Protein 4 in Muscle Ameliorates Muscular Dystrophy through Myostatin and TGFβThe Crystal Structures of Dystrophin and Utrophin Spectrin Repeats: Implications for Domain BoundariesFour and a half LIM protein 1 binds myosin-binding protein C and regulates myosin filament formation and sarcomere assemblyCytoplasmic gamma-actin expression in diverse animal models of muscular dystrophyCytoskeletal tropomyosin Tm5NM1 is required for normal excitation-contraction coupling in skeletal muscleBiomechanics of the sarcolemma and costameres in single skeletal muscle fibers from normal and dystrophin-null miceDestabilization of the dystrophin-glycoprotein complex without functional deficits in alpha-dystrobrevin null muscleChanges in mechanosensitive channel gating following mechanical stimulation in skeletal muscle myotubes from the mdx mouseIdentification of new dystroglycan complexes in skeletal muscleLaminin-6 assembles into multimolecular fibrillar complexes with perlecan and participates in mechanical-signal transduction via a dystroglycan-dependent, integrin-independent mechanismFunctional role of neuroendocrine-specific protein-like 1 in membrane translocation of GLUT4Myopathic changes in murine skeletal muscle lacking syneminTropomodulin isoforms regulate thin filament pointed-end capping and skeletal muscle physiologyEfficient Restoration of the Dystrophin Gene Reading Frame and Protein Structure in DMD Myoblasts Using the CinDel Method.Microutrophin delivery through rAAV6 increases lifespan and improves muscle function in dystrophic dystrophin/utrophin-deficient miceIon-dependent polymerization differences between mammalian beta- and gamma-nonmuscle actin isoformsInteraction of dystrophin rod domain with membrane phospholipids. Evidence of a close proximity between tryptophan residues and lipids.Skeletal muscle-specific ablation of gamma(cyto)-actin does not exacerbate the mdx phenotype.The polyproline site in hinge 2 influences the functional capacity of truncated dystrophins.Hypertrophic stimulation increases beta-actin dynamics in adult feline cardiomyocytesUtrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle.Dynamin-2 mutations linked to Centronuclear Myopathy impair actin-dependent trafficking in muscle cells.Mechanisms of muscle weakness in muscular dystrophyDisease-causing missense mutations in actin binding domain 1 of dystrophin induce thermodynamic instability and protein aggregation.Missense mutations in dystrophin that trigger muscular dystrophy decrease protein stability and lead to cross-beta aggregates.Altered cross-bridge properties in skeletal muscle dystrophiesPredictive urinary biomarkers for steroid-resistant and steroid-sensitive focal segmental glomerulosclerosis using high resolution mass spectrometry and multivariate statistical analysis.Cytoplasmic gamma-actin contributes to a compensatory remodeling response in dystrophin-deficient muscleQuadriceps myopathy caused by skeletal muscle-specific ablation of β(cyto)-actinMechanical effects on KATP channel gating in rat ventricular myocytes.Baraitser-Winter cerebrofrontofacial syndrome: delineation of the spectrum in 42 cases.Cytoplasmic gamma-actin and tropomodulin isoforms link to the sarcoplasmic reticulum in skeletal muscle fibers.Sarcolemma instability during mechanical activity in Largemyd cardiac myocytes with loss of dystroglycan extracellular matrix receptor functionTransgenic overexpression of γ-cytoplasmic actin protects against eccentric contraction-induced force loss in mdx miceExpression of the dystrophin isoform Dp116 preserves functional muscle mass and extends lifespan without preventing dystrophy in severely dystrophic mice
P2860
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P2860
The dystrophin complex forms a mechanically strong link between the sarcolemma and costameric actin
description
2000 nî lūn-bûn
@nan
2000 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2000 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2000年の論文
@ja
2000年論文
@yue
2000年論文
@zh-hant
2000年論文
@zh-hk
2000年論文
@zh-mo
2000年論文
@zh-tw
2000年论文
@wuu
name
The dystrophin complex forms a ...... arcolemma and costameric actin
@ast
The dystrophin complex forms a ...... arcolemma and costameric actin
@en
The dystrophin complex forms a ...... arcolemma and costameric actin
@nl
type
label
The dystrophin complex forms a ...... arcolemma and costameric actin
@ast
The dystrophin complex forms a ...... arcolemma and costameric actin
@en
The dystrophin complex forms a ...... arcolemma and costameric actin
@nl
prefLabel
The dystrophin complex forms a ...... arcolemma and costameric actin
@ast
The dystrophin complex forms a ...... arcolemma and costameric actin
@en
The dystrophin complex forms a ...... arcolemma and costameric actin
@nl
P2093
P2860
P3181
P356
P1476
The dystrophin complex forms a ...... arcolemma and costameric actin
@en
P2093
I N Rybakova
J M Ervasti
P2860
P304
P3181
P356
10.1083/JCB.150.5.1209
P407
P577
2000-09-04T00:00:00Z