The many faces of plectin and plectinopathies: pathology and mechanisms
about
Intermediate filament-associated cytolinker plectin 1c destabilizes microtubules in keratinocytesChemical chaperone ameliorates pathological protein aggregation in plectin-deficient muscle.Neuromuscular synapse integrity requires linkage of acetylcholine receptors to postsynaptic intermediate filament networks via rapsyn-plectin 1f complexes.Determining the mechanical properties of plectin in mouse myoblasts and keratinocytes.MALDI-MSI and label-free LC-ESI-MS/MS shotgun proteomics to investigate protein induction in a murine fibrosarcoma model following treatment with a vascular disrupting agent.Plectin isoform P1b and P1d deficiencies differentially affect mitochondrial morphology and function in skeletal muscle.Absence of Dystrophin Disrupts Skeletal Muscle Signaling: Roles of Ca2+, Reactive Oxygen Species, and Nitric Oxide in the Development of Muscular Dystrophy.Downstream effects of plectin mutations in epidermolysis bullosa simplex with muscular dystrophyLinking cytoarchitecture to metabolism: sarcolemma-associated plectin affects glucose uptake by destabilizing microtubule networks in mdx myofibers.Phosphorylation of serine 4,642 in the C-terminus of plectin by MNK2 and PKA modulates its interaction with intermediate filaments.Emerging roles of sumoylation in the regulation of actin, microtubules, intermediate filaments, and septinsEpidermolysis bullosa simplex in sibling Eurasier dogs is caused by a PLEC non-sense variant.Plectin-intermediate filament partnership in skin, skeletal muscle, and peripheral nerve.Inherited blistering skin diseases: underlying molecular mechanisms and emerging therapies.Anesthetic considerations in myofibrillar myopathy.Biomechanical characterization of myofibrillar myopathies.Desmin in muscle and associated diseases: beyond the structural function.Molecular architecture and function of the hemidesmosome.Blistering disease: insight from the hemidesmosome and other components of the dermal-epidermal junction.Molecular architecture and function of the hemidesmosome.One gene but different proteins and diseases: the complexity of dystonin and bullous pemphigoid antigen 1.Plectin deficiency in liver cancer cells promotes cell migration and sensitivity to sorafenib treatment.Intermediate Filaments and the Plasma Membrane.Lessons from Animal Models of Cytoplasmic Intermediate Filament Proteins.Glu20Ter Variant in PLEC 1f Isoform Causes Limb-Girdle Muscle Dystrophy with Lung Injury.Mutation in exon 1a of PLEC, leading to disruption of plectin isoform 1a, causes autosomal-recessive skin-only epidermolysis bullosa simplex.Epidermolysis bullosa simplex with muscular dystrophy associated with PLEC deletion mutation.Structural proteins of the dermal-epidermal junction targeted by autoantibodies in pemphigoid diseases.Intermediate filaments and cellular mechanics.An Organoruthenium Anticancer Agent Shows Unexpected Target Selectivity For Plectin.GPR56/ADGRG1 regulates development and maintenance of peripheral myelin.Advances in understanding the molecular basis of skin fragility.Zebrafish models of BAG3 myofibrillar myopathy suggest a toxic gain of function leading to BAG3 insufficiency
P2860
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P2860
The many faces of plectin and plectinopathies: pathology and mechanisms
description
2013 nî lūn-bûn
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2013 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
2013 թվականի հունվարին հրատարակված գիտական հոդված
@hy
2013年の論文
@ja
2013年論文
@yue
2013年論文
@zh-hant
2013年論文
@zh-hk
2013年論文
@zh-mo
2013年論文
@zh-tw
2013年论文
@wuu
name
The many faces of plectin and plectinopathies: pathology and mechanisms
@ast
The many faces of plectin and plectinopathies: pathology and mechanisms
@en
The many faces of plectin and plectinopathies: pathology and mechanisms
@nl
type
label
The many faces of plectin and plectinopathies: pathology and mechanisms
@ast
The many faces of plectin and plectinopathies: pathology and mechanisms
@en
The many faces of plectin and plectinopathies: pathology and mechanisms
@nl
prefLabel
The many faces of plectin and plectinopathies: pathology and mechanisms
@ast
The many faces of plectin and plectinopathies: pathology and mechanisms
@en
The many faces of plectin and plectinopathies: pathology and mechanisms
@nl
P2860
P3181
P1476
The many faces of plectin and plectinopathies: pathology and mechanisms
@en
P2093
Lilli Winter
P2860
P2888
P3181
P356
10.1007/S00401-012-1026-0
P407
P577
2013-01-01T00:00:00Z
P6179
1029309430