Hyper immunoglobulin M syndrome due to CD40 deficiency: clinical, molecular, and immunological features
about
Schimke immuno-osseous dysplasia: a clinicopathological correlationPrimary immunodeficiencies associated with eosinophiliaPrevention of infections during primary immunodeficiencyUnbalanced Immune System: Immunodeficiencies and AutoimmunityUpdate on the hyper immunoglobulin M syndromesAutoimmunity in primary T-cell immunodeficiencies.AID in aging and autoimmune diseases.Regulation of the IgE response.Analysis of the association between CD40 and CD40 ligand polymorphisms and systemic sclerosis.Immune activation and a 9-year ongoing complete remission following CD40 antibody therapy and metastasectomy in a patient with metastatic melanoma.Study of association of CD40-CD154 gene polymorphisms with disease susceptibility and cardiovascular risk in Spanish rheumatoid arthritis patients.Persistent Polyclonal B Cell Lymphocytosis B Cells Can Be Activated through CD40-CD154 Interaction.The loss of Gnai2 and Gnai3 in B cells eliminates B lymphocyte compartments and leads to a hyper-IgM like syndrome.Cell surface signaling molecules in the control of immune responses: a tide model.Partial immune reconstitution of X-linked hyper IgM syndrome with recombinant CD40 ligandLongitudinal analysis of antibody response to immunization in paediatric survivors after allogeneic haematopoietic stem cell transplantationPathophysiology of T follicular helper cells in humans and miceCD40 agonist antibody mediated improvement of chronic Cryptosporidium infection in patients with X-linked hyper IgM syndrome.Deleted in Breast Cancer 1 Suppresses B Cell Activation through RelB and Is Regulated by IKKα Phosphorylation.Quorum sensing contributes to activated IgM-secreting B cell homeostasis.Immunity to microbes: lessons from primary immunodeficiencies.A novel polymorphism of the human CD40 receptor with enhanced function.T cell activation inhibitors reduce CD8+ T cell and pro-inflammatory macrophage accumulation in adipose tissue of obese mice.Hyper IgM Syndrome: a Report from the USIDNET RegistryCommon variants at CD40 and other loci confer risk of rheumatoid arthritisTargeting lymphocyte co-stimulation: from bench to bedside.Age effects on B cells and humoral immunity in humans.Aging affects human B cell responses.The hyper IgM syndromes.Clinical, immunological, and molecular characterization of hyper-IgM syndrome due to CD40 deficiency in eleven patients.Autoreactive T cells in the immune pathogenesis of pemphigus vulgaris.B-type suppression: a role played by "regulatory B cells" or "regulatory plasma cells"?Human T Follicular Helper Cells in Primary Immunodeficiency: Quality Just as Important as Quantity.CD40 ligand-mediated activation of the de novo RelB NF-kappaB synthesis pathway in transformed B cells promotes rescue from apoptosis.Late stages of hematopoiesis and B cell lymphopoiesis are regulated by α-synuclein, a key player in Parkinson's disease.Increased serum IgM, immunodeficiency, and autoimmunity: A clinical series.Low levels of NF-κB/p65 mark anergic CD4+ T cells and correlate with disease severity in sarcoidosis.Hyper-immunoglobulin M syndrome type 3 with normal CD40 cell surface expression.Successful haploidentical PBSCT with subsequent T-cell addbacks in a boy with HyperIgM syndrome presenting as severe congenital neutropenia.Comprehensive review of autoantibodies in patients with hyper-IgM syndrome.
P2860
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P2860
Hyper immunoglobulin M syndrome due to CD40 deficiency: clinical, molecular, and immunological features
description
2005 nî lūn-bûn
@nan
2005 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2005 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2005年の論文
@ja
2005年論文
@yue
2005年論文
@zh-hant
2005年論文
@zh-hk
2005年論文
@zh-mo
2005年論文
@zh-tw
2005年论文
@wuu
name
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@ast
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@en
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@nl
type
label
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@ast
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@en
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@nl
prefLabel
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@ast
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@en
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@nl
P2093
P2860
P3181
P1476
Hyper immunoglobulin M syndrom ...... ar, and immunological features
@en
P2093
Alessandro Plebani
Simona Ferrari
Vassilios Lougaris
P2860
P3181
P356
10.1111/J.0105-2896.2005.00229.X
P407
P577
2005-02-01T00:00:00Z