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Serine protease activity and residual LEKTI expression determine phenotype in Netherton syndrome

Serine protease activity and residual LEKTI expression determine phenotype in Netherton syndrome

http://www.wikidata.org/entity/Q28306299

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Matriptase initiates activation of epidermal pro-kallikrein and disease onset in a mouse model of Netherton syndrome Protease and protease-activated receptor-2 signaling in the pathogenesis of atopic dermatitis Molecular Mechanisms of Cutaneous Inflammatory Disorder: Atopic Dermatitis Mechanisms of abnormal lamellar body secretion and the dysfunctional skin barrier in patients with atopic dermatitis Kallikreins 5, 6 and 10 differentially alter pathophysiology and overall survival in an ovarian cancer xenograft model The Skin as a Route of Allergen Exposure: Part I. Immune Components and Mechanisms.Defining the extended substrate specificity of kallikrein 1-related peptidases.Identification of lympho-epithelial Kazal-type inhibitor 2 in human skin as a kallikrein-related peptidase 5-specific protease inhibitor Kallikrein-related peptidase-8 (KLK8) is an active serine protease in human epidermis and sweat and is involved in a skin barrier proteolytic cascade.Skin barrier function Abnormal skin barrier in the etiopathogenesis of atopic dermatitis.Membrane-anchored serine proteases in vertebrate cell and developmental biology Care of the newborn with ichthyosis.Basis for enhanced barrier function of pigmented skin.Sebaceous gland, hair shaft, and epidermal barrier abnormalities in keratosis pilaris with and without filaggrin deficiency Filaggrin genotype in ichthyosis vulgaris predicts abnormalities in epidermal structure and function Comèl-Netherton syndrome defined as primary immunodeficiency.Inhibition of transcription factor specificity protein 1 alters the gene expression profile of keratinocytes leading to upregulation of kallikrein-related peptidases and thymic stromal lymphopoietin.Cellular basis of secondary infections and impaired desquamation in certain inherited ichthyoses Cellular changes that accompany shedding of human corneocytes.Inherited ichthyoses/generalized Mendelian disorders of cornification.Activation profiles of human kallikrein-related peptidases by proteases of the thrombostasis axis Ichthyosis update: towards a function-driven model of pathogenesis of the disorders of cornification and the role of corneocyte proteins in these disorders Basis for the barrier abnormality in atopic dermatitis: outside-inside-outside pathogenic mechanisms A potential role for tissue kallikrein-related peptidases in human cervico-vaginal physiology.Maintenance of an acidic stratum corneum prevents emergence of murine atopic dermatitis.New insights into the functional mechanisms and clinical applications of the kallikrein-related peptidase family.Therapeutic Implications of a Barrier-based Pathogenesis of Atopic Dermatitis.Therapeutic implications of a barrier-based pathogenesis of atopic dermatitis Lipid abnormalities and lipid-based repair strategies in atopic dermatitis.Unleashing the therapeutic potential of human kallikrein-related serine proteases.Betapapillomavirus in multiple non-melanoma skin cancers of Netherton syndrome: Case report and published work review.The Genetics and Epigenetics of Atopic Dermatitis-Filaggrin and Other Polymorphisms.Epidermal barrier in hereditary ichthyoses, atopic dermatitis, and psoriasis.Kallikrein-related peptidases (KLKs) as emerging therapeutic targets: focus on prostate cancer and skin pathologies.Netherton Syndrome: A Genotype-Phenotype Review.Identification of an immunodominant region of the major house dust mite allergen Der p 2 presented by common human leucocyte antigen alleles.Acute acidification of stratum corneum membrane domains using polyhydroxyl acids improves lipid processing and inhibits degradation of corneodesmosomes.Epidermal barrier abnormalities in exfoliative ichthyosis with a novel homozygous loss-of-function mutation in CSTA.[Generalised erythema, scaling and hair anomaly].

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P2860

Serine protease activity and residual LEKTI expression determine phenotype in Netherton syndrome

http://www.wikidata.org/entity/Q28306299

description

2006 nî lūn-bûn

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2006 թուականի Յուլիսին հրատարակուած գիտական յօդուած

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2006 թվականի հուլիսին հրատարակված գիտական հոդված

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2006年の論文

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2006年论文

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Serine protease activity and r ...... henotype in Netherton syndrome

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Arumugam Jayakumar

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Debra Crumrine

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Diane Roseeuw

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Evi Houben

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Fredrik Wagberg

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Gary L Clayman

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Göran Leonardsson

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Jean-Pierre Hachem

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Kenneth R Feingold

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Maria Brattsand

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scholarly article

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10.1038/SJ.JID.5700288

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7

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126

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