Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
about
Novel patient cell-based HTS assay for identification of small molecules for a lysosomal storage diseaseUse of lissamine rhodamine ceramide trihexoside as a functional assay for alpha-galactosidase A in intact cellsLaminin-sulfatide binding initiates basement membrane assembly and enables receptor signaling in Schwann cells and fibroblastsGlobotriaosylceramide induces oxidative stress and up-regulates cell adhesion molecule expression in Fabry disease endothelial cells.High residual arylsulfatase A (ARSA) activity in a patient with late-infantile metachromatic leukodystrophyFunctional compartments of sulphatide metabolism in cultured living cells: evidence for the involvement of a novel sulphatide-degrading pathway.In vivo gene therapy of metachromatic leukodystrophy by lentiviral vectors: correction of neuropathology and protection against learning impairments in affected mice.
P2860
Q28478533-24BCD7E4-B225-4326-B3FE-85B575466068Q34053196-7FD26967-7088-401D-B7AC-104DF90613C2Q36321627-1D2E03DD-FA1D-454A-867D-FFF69147CF2DQ36995447-4F6DC796-8A18-4F36-9784-CBAEF3828CA1Q40539443-61A643F8-329C-4460-A6CB-A613A8C261BBQ41492277-EA0D3C99-73B4-4FEF-8303-6B639CD8626AQ45875261-1F0F175E-615C-44DE-BEBF-FEA7DE0EB475
P2860
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
description
1992 nî lūn-bûn
@nan
1992 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
1992 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
1992年の論文
@ja
1992年論文
@yue
1992年論文
@zh-hant
1992年論文
@zh-hk
1992年論文
@zh-mo
1992年論文
@zh-tw
1992年论文
@wuu
name
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@ast
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@en
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@nl
type
label
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@ast
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@en
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@nl
prefLabel
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@ast
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@en
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@nl
P2093
P1476
Uptake and metabolism of a fluorescent sulfatide analogue in cultured skin fibroblasts
@en
P2093
P356
10.1016/0005-2760(92)90129-J
P407
P577
1992-02-20T00:00:00Z