Specificity of mouse GM2 activator protein and beta-N-acetylhexosaminidases A and B. Similarities and differences with their human counterparts in the catabolism of GM2
about
Animal models of GM2 gangliosidosis: utility and limitationsDegradation of G(M1) and G(M2) by mammalian sialidasesPhotoaffinity labelling of the human GM2-activator protein. Mechanistic insight into ganglioside GM2 degradation.In cellulo examination of a beta-alpha hybrid construct of beta-hexosaminidase A subunits, reported to interact with the GM2 activator protein and hydrolyze GM2 gangliosideProduction of recombinant beta-hexosaminidase A, a potential enzyme for replacement therapy for Tay-Sachs and Sandhoff diseases, in the methylotrophic yeast Ogataea minutaComparative analysis of brain lipids in mice, cats, and humans with Sandhoff diseaseNovel Vector Design and Hexosaminidase Variant Enabling Self-Complementary Adeno-Associated Virus for the Treatment of Tay-Sachs Disease.Metabolic correction in microglia derived from Sandhoff disease model mice.Construction of a hybrid β-hexosaminidase subunit capable of forming stable homodimers that hydrolyze GM2 ganglioside in vivo.Catabolism of asialo-GM2 in man and mouse. Specificity of human/mouse chimeric GM2 activator proteins.
P2860
Q26738663-FC5304D7-A306-42A1-9079-E62A616BB589Q28363347-5ADC666F-5270-44C2-9B1C-86D8BCD8E0A6Q31036440-3E31B6A0-5F15-4858-ADBF-462E1A311981Q34618426-8B61A215-62AD-49CF-8447-6EBA061725BCQ35946763-87815871-7375-4FEA-B0CF-E9D56AE3F4B4Q36650540-84A31D55-130E-43B1-88B6-F172211504D6Q37698337-865F7A39-A09D-42D5-9A25-32DD6C9632ECQ38322339-88645819-6C4A-44F2-90EA-F661771DFABCQ38721702-51DBEF49-5926-4387-8CDB-BF3509DB8FBEQ52536453-99622179-EAE8-4349-B7E8-C2FBCF81D18C
P2860
Specificity of mouse GM2 activator protein and beta-N-acetylhexosaminidases A and B. Similarities and differences with their human counterparts in the catabolism of GM2
description
1998 թուականի Յունուարին հրատարակուած գիտական յօդուած
@hyw
1998 թվականի հունվարին հրատարակված գիտական հոդված
@hy
article publié dans la revue scientifique Journal of Biological Chemistry
@fr
artículu científicu espublizáu en 1998
@ast
im Januar 1998 veröffentlichter wissenschaftlicher Artikel
@de
scientific journal article
@en
vedecký článok (publikovaný 1998/01/02)
@sk
vědecký článek publikovaný v roce 1998
@cs
wetenschappelijk artikel (gepubliceerd op 1998/01/02)
@nl
наукова стаття, опублікована в січні 1998
@uk
name
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@ast
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@en
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@nl
type
label
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@ast
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@en
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@nl
prefLabel
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@ast
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@en
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@nl
P2093
P2860
P3181
P356
P1476
Specificity of mouse GM2 activ ...... parts in the catabolism of GM2
@en
P2093
A. Orlacchio
C. Bertoni
J. A. Yuziuk
T. Beccari
P2860
P3181
P356
10.1074/JBC.273.1.66
P407
P577
1998-01-02T00:00:00Z