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Atrogin-1 and MuRF1 regulate cardiac MyBP-C levels via different mechanismsThe embryological basis of subclinical hypertrophic cardiomyopathyCardiac myosin-binding protein C mutations and hypertrophic cardiomyopathy: haploinsufficiency, deranged phosphorylation, and cardiomyocyte dysfunctionCardiac myosin-binding protein C is required for complete relaxation in intact myocytesNonsense-mediated mRNA decay and ubiquitin-proteasome system regulate cardiac myosin-binding protein C mutant levels in cardiomyopathic miceHow do MYBPC3 mutations cause hypertrophic cardiomyopathy?The ubiquitin-proteasome system and nonsense-mediated mRNA decay in hypertrophic cardiomyopathyAdrenergic stress reveals septal hypertrophy and proteasome impairment in heterozygous Mybpc3-targeted knock-in miceMybpc3 gene therapy for neonatal cardiomyopathy enables long-term disease prevention in miceDefective proteolytic systems in Mybpc3-targeted mice with cardiac hypertrophyThe ubiquitin-proteasome system in cardiac dysfunctionRescue of cardiomyopathy through U7snRNA-mediated exon skipping in Mybpc3-targeted knock-in miceContractile abnormalities and altered drug response in engineered heart tissue from Mybpc3-targeted knock-in miceUbiquitin-proteasome system and hereditary cardiomyopathiesDecreased phosphorylation levels of cardiac myosin-binding protein-C in human and experimental heart failure
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