Further studies on the reconstitution of glucosylceramidase activity by Sap C and anionic phospholipids
about
Crystal structures of saposins A and CReduced cathepsins B and D cause impaired autophagic degradation that can be almost completely restored by overexpression of these two proteases in Sap C-deficient fibroblastsGlucosylceramidase mass and subcellular localization are modulated by cholesterol in Niemann-Pick disease type C.Biosynthesis and degradation of mammalian glycosphingolipids.Saposins utilize two strategies for lipid transfer and CD1 antigen presentationGlucocerebrosidase activity in Parkinson's disease with and without GBA mutationsThe N370S (Asn370-->Ser) mutation affects the capacity of glucosylceramidase to interact with anionic phospholipid-containing membranes and saposin CMembrane lipids regulate ganglioside GM2 catabolism and GM2 activator protein activityInteraction of saposin D with membranes: effect of anionic phospholipids and sphingolipids.Saposin C mutations in Gaucher disease patients resulting in lysosomal lipid accumulation, saposin C deficiency, but normal prosaposin processing and sorting.Saposin B binds and transfers phospholipids.Glucosylceramidase cleaves the glucosidic bond of glucocerebroside to form ceramide
P2860
Q24647618-89BA18A6-CBE3-4C0A-8C2B-A4234363DB0AQ28116738-71F18B41-F1AB-4FB9-8970-643B0F7B6EF0Q34544916-037D02DF-BFB7-4589-945A-20D9394C8E2FQ35153204-3A7C3C8D-6E21-4D08-9D36-32B58C050322Q35849656-3CFE547E-2C97-49E9-BAE6-BB9A3BDB00B1Q36041420-E8C0DC1D-4943-4CFD-9462-3EAD87C006EDQ40436256-8E6A1E60-F090-46BA-B5BE-159FEC25C5CBQ40735884-01040B32-CA9B-4454-BD9A-BC193F6B3737Q41831086-CDC8BA1C-9025-439E-B4EC-F6A677C9325DQ43059581-02C33761-B5F5-4DDA-84F2-C3FB2A766429Q46930833-F73D5922-FBFB-4093-83D4-51A7D5B48136Q50294043-1AF49235-9186-41CF-85AA-961220468411
P2860
Further studies on the reconstitution of glucosylceramidase activity by Sap C and anionic phospholipids
description
2000 թուականի Ապրիլին հրատարակուած գիտական յօդուած
@hyw
2000 թվականի ապրիլին հրատարակված գիտական հոդված
@hy
artículu científicu espublizáu en 2000
@ast
im April 2000 veröffentlichter wissenschaftlicher Artikel
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scientific journal article
@en
vedecký článok (publikovaný 2000/04/21)
@sk
vědecký článek publikovaný v roce 2000
@cs
wetenschappelijk artikel (gepubliceerd op 2000/04/21)
@nl
наукова стаття, опублікована у квітні 2000
@uk
مقالة علمية (نشرت في 21-4-2000)
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name
Further studies on the reconst ...... ap C and anionic phospholipids
@ast
Further studies on the reconst ...... ap C and anionic phospholipids
@en
Further studies on the reconst ...... ap C and anionic phospholipids
@nl
type
label
Further studies on the reconst ...... ap C and anionic phospholipids
@ast
Further studies on the reconst ...... ap C and anionic phospholipids
@en
Further studies on the reconst ...... ap C and anionic phospholipids
@nl
prefLabel
Further studies on the reconst ...... ap C and anionic phospholipids
@ast
Further studies on the reconst ...... ap C and anionic phospholipids
@en
Further studies on the reconst ...... ap C and anionic phospholipids
@nl
P2093
P2860
P1433
P1476
Further studies on the reconst ...... ap C and anionic phospholipids
@en
P2093
A. M. Vaccaro
F. Ciaffoni
R. Salvioli
P2860
P356
10.1016/S0014-5793(00)01417-4
P407
P577
2000-04-21T00:00:00Z