Cardiomyopathy and response to enzyme replacement therapy in a male mouse model for Fabry disease
about
Depletion of globosides and isoglobosides fully reverts the morphologic phenotype of Fabry diseaseAutophagy-lysosome pathway associated neuropathology and axonal degeneration in the brains of alpha-galactosidase A-deficient mice.Multimodality imaging for pre-clinical assessment of Fabry's cardiomyopathy.Tetrahydrobiopterin deficiency in the pathogenesis of Fabry disease.Relative distribution of Gb3 isoforms/analogs in NOD/SCID/Fabry mice tissues determined by tandem mass spectrometry.
P2860
Cardiomyopathy and response to enzyme replacement therapy in a male mouse model for Fabry disease
description
2012 nî lūn-bûn
@nan
2012 թուականին հրատարակուած գիտական յօդուած
@hyw
2012 թվականին հրատարակված գիտական հոդված
@hy
2012年の論文
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2012年論文
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2012年論文
@zh-hant
2012年論文
@zh-hk
2012年論文
@zh-mo
2012年論文
@zh-tw
2012年论文
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name
Cardiomyopathy and response to ...... mouse model for Fabry disease
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Cardiomyopathy and response to ...... mouse model for Fabry disease
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Cardiomyopathy and response to ...... mouse model for Fabry disease
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type
label
Cardiomyopathy and response to ...... mouse model for Fabry disease
@ast
Cardiomyopathy and response to ...... mouse model for Fabry disease
@en
Cardiomyopathy and response to ...... mouse model for Fabry disease
@nl
prefLabel
Cardiomyopathy and response to ...... mouse model for Fabry disease
@ast
Cardiomyopathy and response to ...... mouse model for Fabry disease
@en
Cardiomyopathy and response to ...... mouse model for Fabry disease
@nl
P2093
P2860
P1433
P1476
Cardiomyopathy and response to ...... mouse model for Fabry disease
@en
P2093
Aurelie Nguyen Dinh Cat
Brigitte Escoubet
David G Warnock
Edgar Jaimes
Frederic Jaisser
Trenton Schoeb
Vincent Agrapart
Violaine Griol-Charhbili
Wenguang Feng
P2860
P304
P356
10.1371/JOURNAL.PONE.0033743
P407
P577
2012-01-01T00:00:00Z