OPA1 disease alleles causing dominant optic atrophy have defects in cardiolipin-stimulated GTP hydrolysis and membrane tubulation
about
Dual function of mitochondrial Nm23-H4 protein in phosphotransfer and intermembrane lipid transfer: a cardiolipin-dependent switchSIRT3 deacetylates and activates OPA1 to regulate mitochondrial dynamics during stressAcyl coenzyme A thioesterase Them5/Acot15 is involved in cardiolipin remodeling and fatty liver developmentCardiac and skeletal muscle defects in a mouse model of human Barth syndromeMaking heads or tails of phospholipids in mitochondriaBarth Syndrome: From Mitochondrial Dysfunctions Associated with Aberrant Production of Reactive Oxygen Species to Pluripotent Stem Cell StudiesPlant mitochondrial dynamics and the role of membrane lipidsMitochondrial morphology-emerging role in bioenergeticsPutative biomarkers and targets of estrogen receptor negative human breast cancerMorphological control of mitochondrial bioenergeticsMitochondrial fission: regulation and ER connectionCardiolipin's propensity for phase transition and its reorganization by dynamin-related protein 1 form a basis for mitochondrial membrane fission.Dynamic tubulation of mitochondria drives mitochondrial network formation.Deacylation on the matrix side of the mitochondrial inner membrane regulates cardiolipin remodeling.Membrane tethering and nucleotide-dependent conformational changes drive mitochondrial genome maintenance (Mgm1) protein-mediated membrane fusion.Invited review: Mechanisms of GTP hydrolysis and conformational transitions in the dynamin superfamilyMembrane fission by dynamin: what we know and what we need to knowDisorders of phospholipid metabolism: an emerging class of mitochondrial disease due to defects in nuclear genesRole of mitochondrial lipids in guiding fission and fusionSpecific interaction with cardiolipin triggers functional activation of Dynamin-Related Protein 1Membrane trafficking. Nucleoside diphosphate kinases fuel dynamin superfamily proteins with GTP for membrane remodelingRelease of mitochondrial Opa1 following oxidative stress in HT22 cellsBiosynthesis and roles of phospholipids in mitochondrial fusion, division and mitophagyThe complexity of cardiolipin in health and diseaseCardiolipin at the heart of stress response across kingdomsThe topology and regulation of cardiolipin biosynthesis and remodeling in yeastLoss of OPA1 disturbs cellular calcium homeostasis and sensitizes for excitotoxicity.OPA1 promotes pH flashes that spread between contiguous mitochondria without matrix protein exchangeTransient contraction of mitochondria induces depolarization through the inner membrane dynamin OPA1 protein.The advantage of channeling nucleotides for very processive functionsMitochondrial optic neuropathies - disease mechanisms and therapeutic strategies.The optic nerve: a "mito-window" on mitochondrial neurodegenerationMechanics of dynamin-mediated membrane fission.Shaping the dynamic mitochondrial networkOptic atrophy 1 is an A-kinase anchoring protein on lipid droplets that mediates adrenergic control of lipolysisYeast as a system for modeling mitochondrial disease mechanisms and discovering therapies.Analysis of tubulin alpha-1A/1B C-terminal tail post-translational poly-glutamylation reveals novel modification sites.Acyl-CoA synthetase 1 deficiency alters cardiolipin species and impairs mitochondrial function.Cardiolipin and mitochondrial phosphatidylethanolamine have overlapping functions in mitochondrial fusion in Saccharomyces cerevisiaeGenetic and Clinical Analyses of DOA and LHON in 304 Chinese Patients with Suspected Childhood-Onset Hereditary Optic Neuropathy.
P2860
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P2860
OPA1 disease alleles causing dominant optic atrophy have defects in cardiolipin-stimulated GTP hydrolysis and membrane tubulation
description
2010 nî lūn-bûn
@nan
2010 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2010年の論文
@ja
2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@ast
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@en
type
label
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@ast
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@en
prefLabel
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@ast
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@en
P2093
P2860
P356
P1476
OPA1 disease alleles causing d ...... olysis and membrane tubulation
@en
P2093
David C Chan
Jenny E Hinshaw
Jürgen A W Heymann
Tadato Ban
Zhiyin Song
P2860
P304
P356
10.1093/HMG/DDQ088
P577
2010-02-25T00:00:00Z