Mucopolysaccharidosis IIIB, a lysosomal storage disease, triggers a pathogenic CNS autoimmune response
about
Moving towards effective therapeutic strategies for Neuronal Ceroid LipofuscinosisImmune-Mediated Inflammation May Contribute to the Pathogenesis of Cardiovascular Disease in Mucopolysaccharidosis Type IDefects in the medial entorhinal cortex and dentate gyrus in the mouse model of Sanfilippo syndrome type B.Dysregulation of gene expression in a lysosomal storage disease varies between brain regions implicating unexpected mechanisms of neuropathology.Peripheral nervous system neuropathology and progressive sensory impairments in a mouse model of Mucopolysaccharidosis IIIB.Differential distribution of heparan sulfate glycoforms and elevated expression of heparan sulfate biosynthetic enzyme genes in the brain of mucopolysaccharidosis IIIB mice.Manipulating autophagic processes in autoimmune diseases: a special focus on modulating chaperone-mediated autophagy, an emerging therapeutic target.hsp70 and a novel axis of type I interferon-dependent antiviral immunity in the measles virus-infected brain.Immunologic privilege in the central nervous system and the blood-brain barrier.Altered distribution and function of natural killer cells in murine and human Niemann-Pick disease type C1.Corrective GUSB transfer to the canine mucopolysaccharidosis VII brain.Clinical neurogenetics: neuropathic lysosomal storage disorders.Blood-brain barrier structure and function and the challenges for CNS drug delivery.Mucopolysaccharide diseases: a complex interplay between neuroinflammation, microglial activation and adaptive immunity.Neuroinflammation as modifier of genetically caused neurological disorders of the central nervous system: Understanding pathogenesis and chances for treatment.From Lysosomal Storage Diseases to NKT Cell Activation and BackTiming of Gene Therapy Interventions: The Earlier, the Better.Intracerebroventricular transplantation of human bone marrow-derived multipotent progenitor cells in an immunodeficient mouse model of mucopolysaccharidosis type I (MPS-I).Hyperactivity, unexplained speech delay, and coarse facies--is it Sanfilippo syndrome?
P2860
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P2860
Mucopolysaccharidosis IIIB, a lysosomal storage disease, triggers a pathogenic CNS autoimmune response
description
2010 nî lūn-bûn
@nan
2010 թուականի Յուլիսին հրատարակուած գիտական յօդուած
@hyw
2010 թվականի հուլիսին հրատարակված գիտական հոդված
@hy
2010年の論文
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2010年論文
@yue
2010年論文
@zh-hant
2010年論文
@zh-hk
2010年論文
@zh-mo
2010年論文
@zh-tw
2010年论文
@wuu
name
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@ast
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@en
type
label
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@ast
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@en
prefLabel
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@ast
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@en
P2093
P2860
P356
P1476
Mucopolysaccharidosis IIIB, a ...... ogenic CNS autoimmune response
@en
P2093
Douglas M McCarty
Erin Divers
Julianne Dirosario
Phillip G Popovich
Smruti Killedar
P2860
P2888
P356
10.1186/1742-2094-7-39
P577
2010-07-16T00:00:00Z
P5875
P6179
1032145962