Bestrophin 1 is indispensable for volume regulation in human retinal pigment epithelium cells.
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New Insights on Astrocyte Ion Channels: Critical for Homeostasis and Neuron-Glia SignalingDistribution and Function of the Bestrophin-1 (Best1) Channel in the BrainVolume-regulated anion channel--a frenemy within the brain.Leucine-rich repeat containing protein LRRC8A is essential for swelling-activated Cl- currents and embryonic development in zebrafishBestrophin 1 and retinal disease.Autosomal Recessive Bestrophinopathy Is Not Associated With the Loss of Bestrophin-1 Anion Channel Function in a Patient With a Novel BEST1 MutationThreonine532 phosphorylation in ClC-3 channels is required for angiotensin II-induced Cl(-) current and migration in cultured vascular smooth muscle cells.Coupling of TRPV6 and TMEM16A in epithelial principal cells of the rat epididymis.Mislocalisation of BEST1 in iPSC-derived retinal pigment epithelial cells from a family with autosomal dominant vitreoretinochoroidopathy (ADVIRC)Distinct regions that control ion selectivity and calcium-dependent activation in the bestrophin ion channel.BESTROPHIN1 mutations cause defective chloride conductance in patient stem cell-derived RPE.Biophysics and Physiology of the Volume-Regulated Anion Channel (VRAC)/Volume-Sensitive Outwardly Rectifying Anion Channel (VSOR).Expression of anoctamins in retinal pigment epithelium (RPE).Mechanosensitivity of wild-type and G551D cystic fibrosis transmembrane conductance regulator (CFTR) controls regulatory volume decrease in simple epithelia.Ion channels in regulated cell death.Bestrophinopathy: An RPE-photoreceptor interface disease.Cl- channels in apoptosis.Effects of RPE-conditioned medium on the differentiation of hADSCs into RPE cells, and their proliferation and migration.Patient-specific mutations impair BESTROPHIN1's essential role in mediating Ca2+-dependent Cl- currents in human RPE.Disease modeling studies using induced pluripotent stem cells: are we using enough controls?PHOTORECEPTOR INNER SEGMENT MORPHOLOGY IN BEST VITELLIFORM MACULAR DYSTROPHY.BEST1 protein stability and degradation pathways differ between autosomal dominant Best disease and autosomal recessive bestrophinopathy accounting for the distinct retinal phenotypes.Mutant Best1 Expression and Impaired Phagocytosis in an iPSC Model of Autosomal Recessive Bestrophinopathy.BEST1 gene therapy corrects a diffuse retina-wide microdetachment modulated by light exposure.LRRC8/VRAC anion channels are required for late stages of spermatid development in miceDeficient LRRC8A-dependent volume-regulated anion channel activity is associated with male infertility in mice
P2860
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P2860
Bestrophin 1 is indispensable for volume regulation in human retinal pigment epithelium cells.
description
2015 nî lūn-bûn
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2015 թուականի Մայիսին հրատարակուած գիտական յօդուած
@hyw
2015 թվականի մայիսին հրատարակված գիտական հոդված
@hy
2015年の論文
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2015年論文
@yue
2015年論文
@zh-hant
2015年論文
@zh-hk
2015年論文
@zh-mo
2015年論文
@zh-tw
2015年论文
@wuu
name
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@ast
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@en
type
label
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@ast
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@en
prefLabel
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@ast
Bestrophin 1 is indispensable ...... inal pigment epithelium cells.
@en
P2093
P2860
P50
P356
P1476
Bestrophin 1 is indispensable ...... tinal pigment epithelium cells
@en
P2093
Andrea Milenkovic
Charlotte M Reiff
Franziska Horling
Heinrich Schrewe
Karl Kunzelmann
Lalida Sirianant
Potchanart Wanitchakool
Rainer Schreiber
Stephanie Zimmermann
Thomas Jendryke
P2860
P304
P356
10.1073/PNAS.1418840112
P407
P577
2015-05-04T00:00:00Z