Striatal degeneration and spongy myelinopathy in glutaric acidemia.

Striatal degeneration and spongy myelinopathy in glutaric acidemia.

Item
http://www.wikidata.org/entity/Q30980194
Neonatal astrocyte damage is sufficient to trigger progressive striatal degeneration in a rat model of glutaric acidemia-I.Cerebral haemodynamics in patients with glutaryl-coenzyme A dehydrogenase deficiency.Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiency.Mechanism of age-dependent susceptibility and novel treatment strategy in glutaric acidemia type IA cross-sectional controlled developmental study of neuropsychological functions in patients with glutaric aciduria type I.Dystonia and dyskinesia in glutaric aciduria type I: clinical heterogeneity and therapeutic considerations.[Glutaric aciduria type 1: phenotypic variability. Report of 6 patients]Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.Dynamic changes of striatal and extrastriatal abnormalities in glutaric aciduria type I.Heparan sulfate mediates neuroprotection from degeneration in experimental glutaric aciduria.Striatal neuronal death mediated by astrocytes from the Gcdh-/- mouse model of glutaric acidemia type I.(1)H-MRS in glutaric aciduria type 1: impact of biochemical phenotype and age on the cerebral accumulation of neurotoxic metabolites.Unravelling the complex MRI pattern in glutaric aciduria type I using statistical models-a cohort study in 180 patients.
P2860

Striatal degeneration and spongy myelinopathy in glutaric acidemia.

Item
http://www.wikidata.org/entity/Q30980194
description
1992 nî lūn-bûn
@nan
1992 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
1992 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
1992年の論文
@ja
1992年論文
@yue
1992年論文
@zh-hant
1992年論文
@zh-hk
1992年論文
@zh-mo
1992年論文
@zh-tw
1992年论文
@wuu
name
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@ast
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@en
type
label
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@ast
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@en
prefLabel
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@ast
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@en
P1433
P1476
P2093
P304
P31
P356
P433
P478
P577
P698
P921
P356
P1433
P1476
Striatal degeneration and spongy myelinopathy in glutaric acidemia.
@en
P2093
P304
P31
P356
10.1016/0022-510X(92)90289-W
P433
P478
P577
P698
P921