A little CFTR goes a long way: CFTR-dependent sweat secretion from G551D and R117H-5T cystic fibrosis subjects taking ivacaftor
about
Ivacaftor for patients with cystic fibrosisMarked increases in mucociliary clearance produced by synergistic secretory agonists or inhibition of the epithelial sodium channel.In vivo and in vitro ivacaftor response in cystic fibrosis patients with residual CFTR function: N-of-1 studies.A single amino acid substitution in CFTR converts ATP to an inhibitory ligand.Evaporimeter and Bubble-Imaging Measures of Sweat Gland Secretion Rates.Efficacy and safety of ivacaftor in patients with cystic fibrosis who have an Arg117His-CFTR mutation: a double-blind, randomised controlled trial.The magnitude of ivacaftor effects on fluid secretion via R117H-CFTR channels: Human in vivo measurementsFrom CFTR biology toward combinatorial pharmacotherapy: expanded classification of cystic fibrosis mutations.Low Beta-Adrenergic Sweat Responses in Cystic Fibrosis and Cystic Fibrosis Transmembrane Conductance Regulator-Related Metabolic Syndrome ChildrenCystic fibrosis genetics: from molecular understanding to clinical application.CFTR Modulator Therapies in Pediatric Cystic Fibrosis: Focus on Ivacaftor.An update on new and emerging therapies for cystic fibrosis.Mutation-specific downregulation of CFTR2 variants by gating potentiators.Toward inclusive therapy with CFTR modulators: Progress and challenges.Sweat rate analysis of ivacaftor potentiation of CFTR in non-CF adultsProlonged co-treatment with HGF sustains epithelial integrity and improves pharmacological rescue of Phe508del-CFTR
P2860
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P2860
A little CFTR goes a long way: CFTR-dependent sweat secretion from G551D and R117H-5T cystic fibrosis subjects taking ivacaftor
description
2014 nî lūn-bûn
@nan
2014 թուականի Փետրուարին հրատարակուած գիտական յօդուած
@hyw
2014 թվականի փետրվարին հրատարակված գիտական հոդված
@hy
2014年の論文
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2014年論文
@yue
2014年論文
@zh-hant
2014年論文
@zh-hk
2014年論文
@zh-mo
2014年論文
@zh-tw
2014年论文
@wuu
name
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@ast
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@en
type
label
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@ast
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@en
prefLabel
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@ast
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@en
P2093
P2860
P1433
P1476
A little CFTR goes a long way: ...... osis subjects taking ivacaftor
@en
P2093
Carlos Milla
Colleen Dunn
Eric Frisbee
Ewart A C Thomas
Hyung-Ju Cho
Jeffrey J Wine
Jessica E Char
Jin Hyeok Jeong
Marlene H Wolfe
Richard B Moss
P2860
P304
P356
10.1371/JOURNAL.PONE.0088564
P407
P50
P577
2014-02-10T00:00:00Z