Differential expression of both extracellular and intracellular proteins is involved in the lethal or nonlethal phenotypic variation of BrtlIV, a murine model for osteogenesis imperfecta.
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ER stress-mediated apoptosis in a new mouse model of osteogenesis imperfectaBone composition: relationship to bone fragility and antiosteoporotic drug effectsNanoscale morphology of Type I collagen is altered in the Brtl mouse model of Osteogenesis ImperfectaEvaluation of teriparatide treatment in adults with osteogenesis imperfecta.Chaperoning osteogenesis: new protein-folding disease paradigms.Molecular Consequences of the SERPINH1/HSP47 Mutation in the Dachshund Natural Model of Osteogenesis Imperfecta.Altered cytoskeletal organization characterized lethal but not surviving Brtl+/- mice: insight on phenotypic variability in osteogenesis imperfectaImpaired osteoblastogenesis in a murine model of dominant osteogenesis imperfecta: a new target for osteogenesis imperfecta pharmacological therapy.In utero transplantation of adult bone marrow decreases perinatal lethality and rescues the bone phenotype in the knockin murine model for classical, dominant osteogenesis imperfecta.Makings of a brittle bone: Unexpected lessons from a low protein diet study of a mouse OI model.The unfolded protein response and its relevance to connective tissue diseases.Allele-specific Col1a1 silencing reduces mutant collagen in fibroblasts from Brtl mouse, a model for classical osteogenesis imperfecta.New perspectives on osteogenesis imperfectaThe chaperone activity of 4PBA ameliorates the skeletal phenotype of Chihuahua, a zebrafish model for dominant osteogenesis imperfecta.Cytoskeleton and nuclear lamina affection in recessive osteogenesis imperfecta: A functional proteomics perspective.Cellular mechanism of decreased bone in Brtl mouse model of OI: imbalance of decreased osteoblast function and increased osteoclasts and their precursors.Structural heterogeneity of type I collagen triple helix and its role in osteogenesis imperfecta.Transcriptome analysis of skin fibroblasts with dominant negative COL3A1 mutations provides molecular insights into the etiopathology of vascular Ehlers-Danlos syndrome.4-PBA ameliorates cellular homeostasis in fibroblasts from osteogenesis imperfecta patients by enhancing autophagy and stimulating protein secretion.New frontiers for dominant osteogenesis imperfecta treatment: gene/cellular therapy approachesTreatment options for osteogenesis imperfecta
P2860
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P2860
Differential expression of both extracellular and intracellular proteins is involved in the lethal or nonlethal phenotypic variation of BrtlIV, a murine model for osteogenesis imperfecta.
description
2007 nî lūn-bûn
@nan
2007 թուականի Յունիսին հրատարակուած գիտական յօդուած
@hyw
2007 թվականի հունիսին հրատարակված գիտական հոդված
@hy
2007年の論文
@ja
2007年論文
@yue
2007年論文
@zh-hant
2007年論文
@zh-hk
2007年論文
@zh-mo
2007年論文
@zh-tw
2007年论文
@wuu
name
Differential expression of bot ...... l for osteogenesis imperfecta.
@ast
Differential expression of bot ...... l for osteogenesis imperfecta.
@en
type
label
Differential expression of bot ...... l for osteogenesis imperfecta.
@ast
Differential expression of bot ...... l for osteogenesis imperfecta.
@en
prefLabel
Differential expression of bot ...... l for osteogenesis imperfecta.
@ast
Differential expression of bot ...... l for osteogenesis imperfecta.
@en
P2093
P356
P1433
P1476
Differential expression of bot ...... l for osteogenesis imperfecta.
@en
P2093
Alessandro Armini
Antonella Forlino
Antonio Rossi
Benedetta Gualeni
Chiara Tani
Elena Campari
Giuseppe Cetta
Joan C Marini
P304
P356
10.1002/PMIC.200600919
P577
2007-06-01T00:00:00Z