The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
about
Ammonium accumulation and cell death in a rat 3D brain cell model of glutaric aciduria type IGlutaric acid-mediated apoptosis in primary striatal neuronsA clinical review on megalencephaly: A large brain as a possible sign of cerebral impairment.Mechanistic effects of amino acids and glucose in a novel glutaric aciduria type 1 cell modelEffects of targeted suppression of glutaryl-CoA dehydrogenase by lentivirus-mediated shRNA and excessive intake of lysine on apoptosis in rat striatal neurons.Increased glutamate receptor and transporter expression in the cerebral cortex and striatum of gcdh-/- mice: possible implications for the neuropathology of glutaric acidemia type I.Brain and muscle redox imbalance elicited by acute ethylmalonic acid administration.The use of next-generation sequencing in movement disordersA role of astrocytes in mediating postnatal neurodegeneration in Glutaric acidemia-type 1.Disease-causing mutations affecting surface residues of mitochondrial glutaryl-CoA dehydrogenase impair stability, heteromeric complex formation and mitochondria architecture.Neurotoxic effects of trans-glutaconic acid in rats.Glutaric Aciduria Type 1 and Acute Renal Failure: Case Report and Suggested Pathomechanisms.Oxidative Stress, Disrupted Energy Metabolism, and Altered Signaling Pathways in Glutaryl-CoA Dehydrogenase Knockout Mice: Potential Implications of Quinolinic Acid Toxicity in the Neuropathology of Glutaric Acidemia Type I.White matter injury induced by perinatal exposure to glutaric acid.Low lysine diet in glutaric aciduria type I--effect on anthropometric and biochemical follow-up parameters.Toxic Synergism Between Quinolinic Acid and Glutaric Acid in Neuronal Cells Is Mediated by Oxidative Stress: Insights to a New Toxic Model.α-Ketoadipic Acid and α-Aminoadipic Acid Cause Disturbance of Glutamatergic Neurotransmission and Induction of Oxidative Stress In Vitro in Brain of Adolescent Rats.Two Uneventful Pregnancies in a Woman with Glutaric Aciduria Type 1.Induction of Neuroinflammatory Response and Histopathological Alterations Caused by Quinolinic Acid Administration in the Striatum of Glutaryl-CoA Dehydrogenase Deficient Mice.
P2860
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P2860
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
description
2011 nî lūn-bûn
@nan
2011 թուականի Սեպտեմբերին հրատարակուած գիտական յօդուած
@hyw
2011 թվականի սեպտեմբերին հրատարակված գիտական հոդված
@hy
2011年の論文
@ja
2011年論文
@yue
2011年論文
@zh-hant
2011年論文
@zh-hk
2011年論文
@zh-mo
2011年論文
@zh-tw
2011年论文
@wuu
name
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@ast
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@en
type
label
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@ast
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@en
prefLabel
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@ast
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@en
P2093
P1476
The unsolved puzzle of neuropathogenesis in glutaric aciduria type I.
@en
P2093
Luisa Bonafé
Olivier Braissant
Paris Jafari
P304
P356
10.1016/J.YMGME.2011.08.027
P577
2011-09-02T00:00:00Z